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ICD-10 Guide
DiagnosesAutosomal Dominant Polycystic Kidney Disease

Autosomal Dominant Polycystic Kidney Disease

ICD-10 Coding for Autosomal Dominant Polycystic Kidney Disease(Q61.2, Q61.3)

PRIMARY SPECIALTYNephrology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Autosomal Dominant Polycystic Kidney Disease?
Essential facts and insights about Autosomal Dominant Polycystic Kidney Disease

Key Clinical Considerations:

  • Hypertension
  • Abdominal or flank pain
  • Hematuria
  • Urinary tract infections
  • Progressive renal insufficiency
  • Family history of PKD

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history including family history of PKD
  • Results of imaging studies (ultrasound, CT scan)
  • Laboratory findings (e.g., renal function tests)
  • Physical exam findings (e.g., palpable kidney masses)

Coding Guidelines

Usage Guidelines & Examples

  • Use Q61.3 for confirmed ADPKD; avoid using codes for other types of cystic kidney diseases.
  • Common errors include misclassifying ADPKD as ARPKD.

Code Exclusions

Important Exclusions

  • Autosomal recessive polycystic kidney disease (Q61.2)
  • Acquired cystic kidney disease (N28.1)

Related ICD-10 Codes

Primary Codes
Q61.3
Autosomal dominant polycystic kidney disease
Ancillary Codes
N28.89
Differential Codes
Q61.19
Q61.2
Q61.2
when ADPKD is confirmed.

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Nephrology

Specialty Applications

  • Adults with a family history of ADPKD
  • Nephrology clinics and outpatient settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

What are the documentation requirements?

Document family history, clinical symptoms, and imaging results.

What are the billing considerations?

Ensure accurate coding to reflect the severity and complications of the disease.