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v1.0.0
ICD-10 Guide
DiagnosesKawasaki Disease

Kawasaki Disease

ICD-10 Coding for Kawasaki Disease(M30.3)

PRIMARY SPECIALTYPediatrics
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Kawasaki Disease?
Essential facts and insights about Kawasaki Disease

Key Clinical Considerations:

  • Fever lasting more than 5 days
  • Conjunctival injection
  • Oral mucosal changes (strawberry tongue, cracked lips)
  • Cervical lymphadenopathy
  • Rash (polymorphous, non-vesicular)
  • Peripheral extremity changes (edema, erythema, desquamation)

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history including fever duration and symptoms onset
  • Physical exam findings detailing rash and mucosal changes
  • Laboratory results supporting diagnosis (e.g., elevated inflammatory markers)

Coding Guidelines

Usage Guidelines & Examples

  • Follow ICD-10 guidelines for specificity in coding Kawasaki disease.
  • Common errors include misdiagnosing with other febrile illnesses.

Code Exclusions

Important Exclusions

  • Other vasculitis conditions
  • Alternative codes for febrile illnesses

Related ICD-10 Codes

Primary Codes
I38
Kawasaki disease
Ancillary Codes
I25.41
R50.9
Differential Codes
A48.4
A38.9

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Pediatrics

Specialty Applications

  • Pediatric patients, typically under 5 years of age
  • Outpatient and inpatient pediatric settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

What are the documentation requirements?

Document all clinical criteria met, including duration of fever and specific symptoms.

What are the billing considerations?

Ensure accurate coding to reflect the diagnosis and any associated treatments.