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v1.0.0
ICD-10 Guide
DiagnosesNon Ischemic Cardiomyopathy

Non Ischemic Cardiomyopathy

ICD-10 Coding for Non-Ischemic Cardiomyopathy(I42.8, I42.0)

PRIMARY SPECIALTYCardiology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Non Ischemic Cardiomyopathy?
Essential facts and insights about Non-Ischemic Cardiomyopathy

Key Clinical Considerations:

  • Symptoms include fatigue, shortness of breath, and edema.
  • Echocardiogram showing left ventricular dilation and reduced ejection fraction.
  • Physical exam may reveal jugular venous distension and heart murmurs.

Clinical Information

Clinical Criteria & Documentation Requirements

  • Document patient history, symptoms, and diagnostic test results.
  • Use specific terms like 'non-ischemic cardiomyopathy' and 'dilated cardiomyopathy'.
  • Examples include detailed descriptions of echocardiogram findings and patient symptoms.

Coding Guidelines

Usage Guidelines & Examples

  • Follow guidelines for distinguishing between ischemic and non-ischemic types.
  • Common errors include misclassifying the type of cardiomyopathy.

Code Exclusions

Important Exclusions

  • Ischemic heart disease, hypertrophic cardiomyopathy.
  • ICD codes for ischemic cardiomyopathy (I25.5) and other specific cardiomyopathies.

Related ICD-10 Codes

Primary Codes
I42.0
Dilated cardiomyopathy
I42.9
Cardiomyopathy, unspecified
Ancillary Codes
I50.9
Differential Codes
I42.9
I42.9
only when no specific type of cardiomyopathy is documented.

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Cardiology

Specialty Applications

  • Adults with heart failure symptoms, patients with a history of myocarditis or genetic predisposition.
  • Cardiology clinics, hospitals, and outpatient settings.

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

Documentation requirements?

Include detailed patient history, symptoms, and diagnostic findings.

Billing considerations?

Ensure accurate coding to reflect the specific type of cardiomyopathy for reimbursement.