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v1.0.0
ICD-10 Guide
DiagnosesPolycythaemia

Polycythaemia

ICD-10 Coding for Polycythaemia(D45, D75.0, D75.1)

PRIMARY SPECIALTYHematology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Polycythaemia?
Essential facts and insights about Polycythaemia

Key Clinical Considerations:

  • Elevated hemoglobin or hematocrit levels
  • Bone marrow biopsy showing hypercellularity
  • Symptoms such as headache, dizziness, and visual disturbances

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history including symptoms and duration
  • Laboratory results for hemoglobin and hematocrit levels
  • Assessment of secondary causes of polycythaemia

Coding Guidelines

Usage Guidelines & Examples

  • Use D45 for primary polycythemia vera and D47.1 for secondary causes.
  • Common errors include misclassifying secondary causes as primary.

Code Exclusions

Important Exclusions

  • Secondary causes such as chronic hypoxia or tumors producing erythropoietin
  • Alternative codes for other hematological disorders

Related ICD-10 Codes

Primary Codes
D45
Polycythemia vera
D47.1
Secondary polycythemia
Differential Codes
D75.0
D75.1
D45
K2
mutation and bone marrow findings.

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Hematology

Specialty Applications

  • Adults with symptoms of increased blood viscosity
  • Hematology clinics and general practice settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

What are the documentation requirements?

Document patient history, lab results, and any secondary causes.

What are the billing considerations?

Ensure accurate coding based on primary vs secondary polycythaemia.