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v1.0.0
ICD-10 Guide
DiagnosesRetroperitoneal Fibrosis

Retroperitoneal Fibrosis

ICD-10 Coding for Retroperitoneal Fibrosis(K68.2, N13.5)

PRIMARY SPECIALTYRadiology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Retroperitoneal Fibrosis?
Essential facts and insights about Retroperitoneal Fibrosis

Key Clinical Considerations:

  • Abdominal pain or discomfort
  • Weight loss
  • Renal impairment
  • Key diagnostic tests include CT or MRI showing a mass in the retroperitoneum
  • Physical exam may reveal abdominal tenderness or a palpable mass

Clinical Information

Clinical Criteria & Documentation Requirements

  • Document patient history, symptoms, and physical exam findings
  • Use specific terms like 'retroperitoneal fibrosis' or 'Ormond's disease'
  • Examples include detailed imaging reports and clinical notes describing symptoms and findings

Coding Guidelines

Usage Guidelines & Examples

  • Follow guidelines for coding fibrosis versus other abdominal masses
  • Common errors include misclassifying the condition as a neoplasm

Code Exclusions

Important Exclusions

  • Malignant tumors of the retroperitoneum
  • Other forms of fibrosis not related to the retroperitoneum

Related ICD-10 Codes

Primary Codes
M49.2
Retroperitoneal fibrosis
Ancillary Codes
N13.5
Differential Codes
C78.6

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Radiology

Specialty Applications

  • Adult patients, particularly those over 50
  • Radiology departments and outpatient imaging centers

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

Documentation requirements?

Include detailed imaging findings and clinical correlation.

Billing considerations?

Ensure accurate coding to reflect the complexity of the condition.