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v1.0.0
ICD-10 Guide
DiagnosesVasculitis

Vasculitis

ICD-10 Coding for Vasculitis(I77.6, I77.8, L95.0)

PRIMARY SPECIALTYRheumatology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Vasculitis?
Essential facts and insights about Vasculitis

Key Clinical Considerations:

  • Fever, malaise, weight loss, and arthralgia
  • Elevated inflammatory markers (ESR, CRP), biopsy showing vasculitis
  • Skin rashes, joint swelling, and organ-specific symptoms

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history, physical exam findings, laboratory results, and imaging studies
  • ICD-10-CM codes for specific types of vasculitis (e.g., M30-M36)
  • Examples: 'Patient presents with systemic symptoms and elevated ESR, biopsy confirms vasculitis.'

Coding Guidelines

Usage Guidelines & Examples

  • Follow guidelines for distinguishing between primary and secondary vasculitis.
  • Common errors include misclassifying the type of vasculitis or omitting necessary documentation.

Code Exclusions

Important Exclusions

  • Conditions such as infections or malignancies that may mimic vasculitis
  • Alternative codes for related but distinct conditions (e.g., M05 for rheumatoid arthritis with vasculitis)

Related ICD-10 Codes

Primary Codes
M30.0
Kawasaki disease
M31.0
Hypersensitivity vasculitis
M31.1
Wegener's granulomatosis
M31.2
Churg-Strauss syndrome
M31.3
Polyarteritis nodosa
Ancillary Codes
N18.9
Differential Codes
L95.9
L95.9
only if vasculitis is limited to the skin.
I77.6
I77.6
if no specific organ involvement is documented.

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Rheumatology

Specialty Applications

  • Adults and children with autoimmune diseases, systemic inflammatory conditions
  • Rheumatology clinics, emergency departments, and outpatient settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

Documentation requirements?

Include detailed patient history, lab results, and imaging findings.

Billing considerations?

Ensure accurate coding to reflect the specific type of vasculitis for proper reimbursement.