Other Creutzfeldt-Jakob disease
ICD-10 A81.09 is a billable code used to indicate a diagnosis of other creutzfeldt-jakob disease.
Creutzfeldt-Jakob disease (CJD) is a rare and fatal neurodegenerative disorder caused by prions, which are misfolded proteins that induce abnormal folding of normal cellular proteins in the brain. Other Creutzfeldt-Jakob disease (A81.09) refers to forms of CJD that do not fall under the classic categories of sporadic, familial, or iatrogenic CJD. Symptoms typically include rapidly progressive dementia, ataxia, myoclonus, and visual disturbances. The disease is characterized by spongiform changes in the brain, leading to severe neurological impairment. Diagnosis is often challenging and relies on clinical evaluation, MRI findings, and cerebrospinal fluid analysis for the presence of 14-3-3 protein. Given the prion nature of the disease, there is no effective treatment, and management focuses on supportive care. Vaccination status is not directly related to CJD, but understanding the patient's overall health and vaccination history can be important in differential diagnosis and management of neurological complications.
Comprehensive neurological examination findings, imaging results, and laboratory test results.
Patients presenting with rapidly progressive dementia and neurological deficits.
Ensure all diagnostic criteria are met and documented, including exclusion of other conditions.
History of exposure to prion diseases, detailed patient history, and laboratory findings.
Patients with suspected prion disease due to exposure history or atypical neurological symptoms.
Consideration of other infectious causes of neurological symptoms and thorough documentation of exposure history.
Used for follow-up visits in patients with diagnosed CJD.
Detailed history and examination findings must be documented.
Neurology specialists should ensure comprehensive documentation of neurological assessments.
Common symptoms include rapidly progressive dementia, ataxia, myoclonus, and visual disturbances. Patients may also experience personality changes and other neurological deficits.
