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v1.0.0
ICD-10 Guide
ICD-10 CodesD18.1

D18.1

Billable

Lymphangioma, any site

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/05/2025

Code Description

ICD-10 D18.1 is a billable code used to indicate a diagnosis of lymphangioma, any site.

Key Diagnostic Point:

Lymphangiomas are benign tumors that arise from the lymphatic vessels and can occur in various anatomical locations, including the skin, subcutaneous tissue, and deeper structures. These neoplasms are characterized by the proliferation of lymphatic endothelial cells, leading to the formation of cystic or solid masses filled with lymphatic fluid. Lymphangiomas are most commonly diagnosed in children, although they can occur at any age. Clinically, they may present as soft, compressible swellings that can vary in size and may be associated with other vascular anomalies. While lymphangiomas are generally benign, they can cause complications depending on their size and location, such as obstruction of lymphatic drainage or cosmetic concerns. Surveillance is often recommended to monitor for changes in size or symptoms, particularly in cases where the lymphangioma is located near vital structures. Although malignant transformation is rare, there is a potential for lymphangiomas to be associated with other malignancies, necessitating careful evaluation and management.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and location of lymphangiomas
  • Differentiation from other vascular lesions
  • Potential for associated conditions requiring additional coding
  • Need for precise documentation of size and symptoms

Audit Risk Factors

  • Inadequate documentation of the size and location of the lymphangioma
  • Failure to document associated symptoms or complications
  • Misclassification as a malignant neoplasm
  • Lack of follow-up documentation for surveillance

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Detailed history and physical examination notes, including size, location, and symptoms of the lymphangioma.

Common Clinical Scenarios

Diagnosis of lymphangioma in infants or children presenting with soft tissue masses.

Billing Considerations

Consideration of growth patterns and potential for intervention.

Dermatology

Documentation Requirements

Photographic evidence of lesions, detailed descriptions of the morphology and location.

Common Clinical Scenarios

Evaluation of cutaneous lymphangiomas and their management.

Billing Considerations

Documentation of cosmetic concerns and treatment options.

Coding Guidelines

Inclusion Criteria

Use D18.1 When
  • According to ICD
  • 10 coding guidelines, D18
  • 1 should be used for lymphangiomas that are confirmed through clinical evaluation
  • It is important to document the specific site and any associated symptoms

Exclusion Criteria

Do NOT use D18.1 When
  • Exclusion criteria include malignant lymphatic tumors, which should be coded differently

Related ICD-10 Codes

Related CPT Codes

38792CPT Code

Lymphatic imaging

Clinical Scenario

Used for diagnostic evaluation of lymphangiomas.

Documentation Requirements

Document the indication for imaging and findings.

Specialty Considerations

Pediatric specialists may require additional imaging for growth monitoring.

11400CPT Code

Excision, benign skin lesion

Clinical Scenario

Surgical excision of a lymphangioma.

Documentation Requirements

Document the size, location, and reason for excision.

Specialty Considerations

Ensure clear documentation of the surgical approach and pathology results.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of lymphangiomas, improving the accuracy of data collection and reimbursement processes. The detailed descriptions in ICD-10 facilitate better understanding and management of these conditions.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of lymphangiomas, improving the accuracy of data collection and reimbursement processes. The detailed descriptions in ICD-10 facilitate better understanding and management of these conditions.

Reimbursement & Billing Impact

reimbursement processes. The detailed descriptions in ICD-10 facilitate better understanding and management of these conditions.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What is the typical treatment for lymphangioma?

Treatment options for lymphangioma may include observation, sclerotherapy, or surgical excision, depending on the size, location, and symptoms associated with the lesion.

Can lymphangiomas become malignant?

While lymphangiomas are benign, there is a rare potential for them to be associated with malignancies, necessitating careful monitoring and evaluation.