Desmoid tumor, intrathoracic
ICD-10 D48.112 is a billable code used to indicate a diagnosis of desmoid tumor, intrathoracic.
Desmoid tumors, also known as aggressive fibromatosis, are benign neoplasms that arise from connective tissue and are characterized by their infiltrative growth pattern. Intrathoracic desmoid tumors specifically occur within the thoracic cavity, which can include the pleura, mediastinum, or chest wall. These tumors are classified under neoplasms of uncertain behavior, meaning they do not metastasize like malignant tumors but can exhibit aggressive local behavior, leading to significant morbidity. The etiology of desmoid tumors is often associated with genetic predispositions, particularly in patients with familial adenomatous polyposis (FAP). Clinically, patients may present with chest pain, respiratory symptoms, or incidental findings on imaging studies. Surveillance is critical due to the potential for local recurrence after surgical excision, and management may include observation, surgical resection, or systemic therapies. The unpredictable nature of desmoid tumors necessitates careful monitoring and a multidisciplinary approach to treatment, particularly in the context of their uncertain behavior and potential for progression.
Detailed pathology reports, imaging studies, and treatment plans.
Management of desmoid tumors post-surgery, monitoring for recurrence.
Ensure clarity in the tumor's behavior and treatment response.
Operative reports detailing tumor excision and margins.
Surgical intervention for symptomatic desmoid tumors.
Documenting the rationale for surgical decisions and follow-up care.
Used when a desmoid tumor is located in the breast area.
Operative report detailing the procedure and tumor characteristics.
Oncology specialists should document tumor behavior and follow-up care.
Desmoid tumors are benign but can be locally aggressive. Prognosis varies based on tumor location and treatment response, with a risk of recurrence after treatment.
