Hb-SS disease with acute chest syndrome
ICD-10 D57.01 is a billable code used to indicate a diagnosis of hb-ss disease with acute chest syndrome.
Hb-SS disease, also known as sickle cell disease, is a genetic blood disorder characterized by the presence of hemoglobin S (HbS), which causes red blood cells to become rigid and sickle-shaped. This abnormal shape leads to various complications, including hemolytic anemia, vaso-occlusive crises, and acute chest syndrome (ACS). ACS is a severe complication of sickle cell disease, presenting with chest pain, fever, cough, and respiratory distress, often due to pulmonary infarction or infection. The pathophysiology involves sickling of red blood cells in the pulmonary vasculature, leading to impaired oxygenation and inflammation. Patients with Hb-SS disease are at increased risk for infections, particularly from encapsulated organisms, due to splenic dysfunction. Management of ACS typically involves supportive care, pain management, and sometimes blood transfusions or hydroxyurea therapy. Accurate coding of D57.01 is crucial for proper reimbursement and tracking of healthcare outcomes related to this serious condition.
Detailed patient history, laboratory results, and treatment plans.
Management of sickle cell crises, blood transfusions, and complications like ACS.
Need for comprehensive documentation of genetic testing and patient education.
Pulmonary function tests, imaging studies, and treatment responses.
Evaluation and management of respiratory symptoms in sickle cell patients.
Documentation of acute respiratory distress and differentiation from other lung diseases.
Used when a patient with Hb-SS disease requires a blood transfusion due to acute chest syndrome.
Document the indication for transfusion and the patient's response.
Hematology specialists should ensure compliance with transfusion protocols.
Coding D57.01 is crucial for identifying patients with Hb-SS disease who experience acute chest syndrome, allowing for appropriate management and tracking of healthcare outcomes.
