Hb-SS disease with splenic sequestration
ICD-10 D57.02 is a billable code used to indicate a diagnosis of hb-ss disease with splenic sequestration.
Hb-SS disease, commonly known as sickle cell disease, is a genetic blood disorder characterized by the presence of hemoglobin S (HbS). In patients with Hb-SS disease, the red blood cells become rigid and sickle-shaped, leading to various complications, including hemolytic anemia, pain crises, and organ damage. Splenic sequestration occurs when sickled red blood cells obstruct blood flow in the spleen, causing acute splenic enlargement and a sudden drop in hemoglobin levels. This condition can lead to severe anemia and requires prompt medical intervention. Patients may present with symptoms such as abdominal pain, pallor, fatigue, and signs of shock. The management of splenic sequestration often involves hydration, pain management, and sometimes blood transfusions. Genetic factors play a crucial role in the disease, as it is inherited in an autosomal recessive pattern. Understanding the pathophysiology of Hb-SS disease and its complications is essential for effective treatment and coding.
Detailed clinical notes on hemoglobin levels, splenic size, and patient history.
Management of acute splenic sequestration, chronic pain management, and transfusion therapy.
Ensure comprehensive documentation of all episodes of splenic sequestration and related treatments.
Growth and development assessments, family history of sickle cell disease.
Routine check-ups for children with Hb-SS disease, management of pain crises.
Monitor for developmental delays and ensure family education on disease management.
Used during acute management of splenic sequestration.
Document the reason for transfusion and patient response.
Hematology specialists should ensure that transfusion protocols are followed.
Coding D57.02 accurately reflects the patient's condition of Hb-SS disease with splenic sequestration, which is critical for appropriate treatment, management, and reimbursement.
