Sickle-cell/Hb-C disease with acute chest syndrome
ICD-10 D57.211 is a billable code used to indicate a diagnosis of sickle-cell/hb-c disease with acute chest syndrome.
Sickle-cell/Hb-C disease with acute chest syndrome is a severe complication of sickle cell disease characterized by the presence of sickle-shaped red blood cells and hemoglobin C. Acute chest syndrome is defined by the acute onset of chest pain, fever, and respiratory symptoms, often accompanied by pulmonary infiltrates on imaging. This condition arises due to vaso-occlusive crises that lead to ischemia and inflammation in the lungs, resulting in impaired gas exchange and respiratory distress. Patients may present with symptoms such as cough, shortness of breath, and hypoxia. The underlying pathophysiology involves hemolytic anemia due to the destruction of sickle cells, which can lead to increased bilirubin levels and potential complications like gallstones. Genetic factors play a significant role, as sickle cell disease is inherited in an autosomal recessive pattern, requiring both parents to pass on the sickle cell trait. Management often includes supportive care, pain management, and in some cases, blood transfusions or hydroxyurea therapy to reduce the frequency of crises.
Detailed clinical history, laboratory results, and imaging studies must be documented.
Management of patients with recurrent vaso-occlusive crises and acute chest syndrome.
Ensure that all acute symptoms are documented and linked to the sickle cell diagnosis.
Pulmonary function tests, imaging results, and treatment plans for respiratory symptoms.
Evaluation and management of acute chest syndrome in patients with sickle cell disease.
Documentation should clearly outline the respiratory assessment and interventions performed.
Used when a patient with sickle cell disease requires a blood transfusion due to acute chest syndrome.
Document the indication for transfusion and the patient's response.
Hematology specialists should ensure that the transfusion is justified based on clinical need.
Coding D57.211 accurately reflects the severity of the patient's condition, ensuring appropriate treatment and reimbursement for the complexities involved in managing sickle cell disease with acute chest syndrome.
