Sickle-cell/Hb-C disease with dactylitis
ICD-10 D57.214 is a billable code used to indicate a diagnosis of sickle-cell/hb-c disease with dactylitis.
Sickle-cell/Hb-C disease with dactylitis is a specific type of hemolytic anemia characterized by the presence of both sickle hemoglobin (HbS) and hemoglobin C (HbC). This condition arises from a genetic mutation in the beta-globin gene, leading to the production of abnormal hemoglobin that distorts red blood cells into a sickle shape. Dactylitis, or hand-foot syndrome, is a common complication in children with sickle cell disease, resulting from vaso-occlusive crises that cause painful swelling of the fingers and toes. Patients may experience recurrent episodes of pain, anemia, and increased susceptibility to infections due to splenic dysfunction. Management often includes pain control, hydration, and in some cases, blood transfusions or hydroxyurea therapy to reduce the frequency of crises. Genetic counseling is also recommended for affected individuals and their families to understand inheritance patterns and risks for offspring. Regular monitoring and comprehensive care are essential to manage complications and improve quality of life.
Detailed clinical history, laboratory results, and treatment plans.
Management of pain crises, blood transfusions, and monitoring for complications.
Documentation must clearly indicate the presence of dactylitis and its impact on treatment.
Growth and development assessments, vaccination history, and family history of hemoglobinopathies.
Routine check-ups, management of acute pain episodes, and education on disease management.
Focus on developmental milestones and psychosocial aspects of living with a chronic condition.
Used when a patient with sickle-cell disease requires a blood transfusion due to severe anemia.
Document the reason for transfusion, patient’s hemoglobin levels, and any adverse reactions.
Hematology specialists should ensure that transfusion protocols are followed.
Dactylitis is often one of the first signs of sickle-cell disease in children, indicating vaso-occlusive crises and the need for early intervention and management.
