Sickle-cell thalassemia, unspecified, with acute chest syndrome
ICD-10 D57.411 is a billable code used to indicate a diagnosis of sickle-cell thalassemia, unspecified, with acute chest syndrome.
Sickle-cell thalassemia is a genetic blood disorder characterized by the presence of both sickle cell disease and thalassemia, leading to abnormal hemoglobin production. Patients with this condition often experience hemolytic anemia due to the destruction of sickle-shaped red blood cells, which can lead to various complications, including acute chest syndrome. Acute chest syndrome is a severe complication that presents with chest pain, fever, and respiratory symptoms, often triggered by infection, pulmonary fat embolism, or vaso-occlusive crises. The combination of sickle cell disease and thalassemia can exacerbate the severity of symptoms and complications, making management challenging. Patients may require frequent blood transfusions, pain management, and close monitoring for respiratory distress. Genetic factors play a significant role in the manifestation of this condition, as both sickle cell disease and thalassemia are inherited disorders. Accurate coding is essential for appropriate treatment and management of these patients, as well as for tracking healthcare outcomes and resource utilization.
Detailed patient history, laboratory results, and treatment plans must be documented.
Management of acute chest syndrome, blood transfusions, and pain crises.
Ensure that all genetic testing results and family history are included in the documentation.
Documentation of respiratory symptoms, imaging studies, and treatment responses.
Evaluation and management of respiratory distress in patients with acute chest syndrome.
Document any interventions such as bronchodilator therapy or oxygen supplementation.
Used during acute management of sickle-cell thalassemia with acute chest syndrome.
Document the indication for transfusion and patient response.
Hematology specialists should ensure compliance with transfusion protocols.
Coding D57.411 accurately reflects the complexity of managing patients with both sickle-cell thalassemia and acute chest syndrome, ensuring appropriate treatment and resource allocation.
