Other sickle-cell disorders with crisis
ICD-10 D57.81 is a billable code used to indicate a diagnosis of other sickle-cell disorders with crisis.
D57.81 refers to other sickle-cell disorders characterized by recurrent vaso-occlusive crises, which can lead to acute pain episodes and various complications. Sickle-cell disorders are a group of inherited red blood cell disorders that result from mutations in the HBB gene, leading to the production of abnormal hemoglobin known as hemoglobin S (HbS). In these disorders, the sickle-shaped red blood cells can obstruct blood flow, causing ischemia and pain. Patients may experience hemolytic anemia due to the rapid destruction of sickle cells, leading to fatigue, pallor, and jaundice. Enzyme deficiencies, such as glucose-6-phosphate dehydrogenase deficiency, can exacerbate hemolysis and crisis episodes. Thalassemias, another group of inherited blood disorders, may coexist with sickle-cell disease, complicating the clinical picture. Genetic factors play a crucial role in the severity and frequency of crises, with some patients experiencing more frequent episodes due to additional genetic mutations. Accurate coding of D57.81 is essential for proper management and treatment of these patients, as it reflects the complexity of their condition and the need for tailored therapeutic approaches.
Detailed patient history, laboratory results, and genetic testing documentation.
Management of vaso-occlusive crises, blood transfusions, and hydroxyurea therapy.
Ensure documentation reflects the specific type of sickle-cell disorder and any associated complications.
Genetic testing results and family history of sickle-cell disorders.
Counseling patients on genetic risks and implications of sickle-cell disorders.
Accurate coding requires understanding of genetic mutations and their impact on disease severity.
Used during management of severe anemia or crisis.
Document the reason for transfusion and patient response.
Hematology specialists should ensure proper indication for transfusion is documented.
D57.81 is used for other sickle-cell disorders with crisis, while D57.0 specifically refers to sickle-cell disease with crisis. Accurate coding depends on the specific diagnosis and clinical presentation.
