Von Willebrand disease, type 1
ICD-10 D68.01 is a billable code used to indicate a diagnosis of von willebrand disease, type 1.
Von Willebrand disease (VWD) type 1 is the most common hereditary bleeding disorder, characterized by a deficiency or dysfunction of von Willebrand factor (VWF), a protein crucial for platelet adhesion and aggregation. Patients with type 1 VWD typically present with mild to moderate bleeding symptoms, including easy bruising, prolonged bleeding from cuts, and heavy menstrual bleeding in women. The severity of symptoms correlates with the level of VWF in the blood. Diagnosis is confirmed through laboratory tests measuring VWF levels and activity, as well as factor VIII levels, which are often low in VWD. Management may include desmopressin (DDAVP) to stimulate the release of VWF from endothelial cells, and in more severe cases, VWF concentrates may be necessary. Understanding the coagulation cascade and the role of VWF is essential for managing patients with this condition, as it can overlap with other bleeding disorders such as hemophilia and thrombocytopenia.
Detailed patient history, including bleeding episodes and family history, laboratory test results, and treatment plans.
Patients presenting with unexplained bleeding, preoperative assessments for surgical procedures, and management of bleeding during pregnancy.
Consideration of other bleeding disorders and the need for interdisciplinary collaboration for comprehensive care.
Menstrual history, obstetric history, and any bleeding complications during pregnancy.
Management of heavy menstrual bleeding and bleeding complications during labor.
Coordination with hematology for preconception counseling and management during pregnancy.
Used to evaluate bleeding disorders, including VWD.
Document the indication for the CBC and any relevant clinical findings.
Hematology specialists should ensure comprehensive evaluation of bleeding risk.
The primary treatment for Von Willebrand disease type 1 is desmopressin (DDAVP), which stimulates the release of von Willebrand factor from endothelial cells, increasing levels in the bloodstream.
