Von Willebrand disease, type 2M
ICD-10 D68.022 is a billable code used to indicate a diagnosis of von willebrand disease, type 2m.
Von Willebrand disease (VWD) is a genetic bleeding disorder characterized by a deficiency or dysfunction of von Willebrand factor (VWF), a protein crucial for platelet adhesion and aggregation. Type 2M is a subtype of VWD where there is a qualitative defect in VWF, leading to impaired platelet function despite normal levels of the factor. Patients with type 2M often present with mucosal bleeding, easy bruising, and prolonged bleeding after injury or surgery. The condition can be exacerbated by certain medications, such as aspirin, which can further inhibit platelet function. Diagnosis typically involves laboratory tests that assess VWF levels and function, including ristocetin cofactor activity and VWF antigen levels. Management may include desmopressin (DDAVP) to stimulate the release of VWF from endothelial cells, along with factor replacement therapy in more severe cases. Understanding the nuances of VWD type 2M is essential for effective treatment and management of bleeding episodes.
Comprehensive lab results, patient history, and treatment plans.
Patients presenting with unexplained bleeding, pre-operative assessments.
Ensure accurate documentation of VWF levels and function tests.
Detailed accounts of bleeding episodes and interventions performed.
Management of acute bleeding episodes in patients with known VWD.
Document any anticoagulant use and its impact on bleeding risk.
Used for laboratory testing to confirm VWD.
Document the reason for blood draw and any relevant patient history.
Ensure that the specialty performing the test is noted.
The primary treatment for Von Willebrand disease type 2M often includes desmopressin (DDAVP), which stimulates the release of von Willebrand factor from endothelial cells, increasing its levels in the bloodstream.
