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ICD-10 Guide
ICD-10 CodesD68.04

D68.04

Billable

Acquired von Willebrand disease

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/05/2025

Code Description

ICD-10 D68.04 is a billable code used to indicate a diagnosis of acquired von willebrand disease.

Key Diagnostic Point:

Acquired von Willebrand disease (AvWD) is a bleeding disorder characterized by a deficiency or dysfunction of von Willebrand factor (vWF), which is crucial for platelet adhesion and aggregation during hemostasis. Unlike hereditary forms of von Willebrand disease, AvWD typically arises secondary to other medical conditions, such as autoimmune disorders, malignancies, or certain medications. Patients may present with symptoms such as easy bruising, prolonged bleeding from cuts, heavy menstrual periods, and spontaneous bleeding episodes. Diagnosis often involves laboratory tests that assess vWF levels and function, platelet counts, and coagulation profiles. Treatment focuses on addressing the underlying condition and may include desmopressin, factor replacement therapy, or antifibrinolytics. Understanding the nuances of AvWD is essential for effective management and coding, as it can significantly impact patient outcomes and healthcare costs.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Differentiation from hereditary forms of von Willebrand disease
  • Need for comprehensive patient history to identify underlying causes
  • Potential overlap with other bleeding disorders like hemophilia
  • Variability in clinical presentation and laboratory findings

Audit Risk Factors

  • Inadequate documentation of the underlying condition causing AvWD
  • Failure to specify the type of acquired von Willebrand disease
  • Misclassification with other bleeding disorders
  • Lack of supporting lab results in the medical record

Specialty Focus

Medical Specialties

Hematology

Documentation Requirements

Detailed lab results, patient history, and treatment plans must be documented.

Common Clinical Scenarios

Patients presenting with unexplained bleeding, bruising, or abnormal lab results.

Billing Considerations

Ensure accurate documentation of vWF levels and function tests.

Internal Medicine

Documentation Requirements

Comprehensive assessment of comorbid conditions and medications.

Common Clinical Scenarios

Patients with autoimmune diseases or malignancies presenting with bleeding symptoms.

Billing Considerations

Document any medications that may contribute to bleeding risk.

Coding Guidelines

Inclusion Criteria

Use D68.04 When
  • Follow the official ICD
  • CM coding guidelines, ensuring that the code is used only when the condition is confirmed as acquired and not hereditary
  • Document any underlying conditions that contribute to the diagnosis

Exclusion Criteria

Do NOT use D68.04 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

85384CPT Code

Factor VIII and von Willebrand factor antigen

Clinical Scenario

Used to assess vWF levels in patients suspected of having AvWD.

Documentation Requirements

Document the reason for testing and any relevant clinical findings.

Specialty Considerations

Hematology specialists should ensure comprehensive lab results are included.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of acquired conditions like AvWD, improving the accuracy of diagnoses and treatment plans. This specificity aids in better tracking of disease prevalence and treatment outcomes.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of acquired conditions like AvWD, improving the accuracy of diagnoses and treatment plans. This specificity aids in better tracking of disease prevalence and treatment outcomes.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for more specific coding of acquired conditions like AvWD, improving the accuracy of diagnoses and treatment plans. This specificity aids in better tracking of disease prevalence and treatment outcomes.

Resources

Clinical References

  • •
    National Hemophilia Foundation

Coding & Billing References

  • •
    National Hemophilia Foundation

Frequently Asked Questions

What is the primary cause of acquired von Willebrand disease?

AvWD is often caused by underlying conditions such as autoimmune disorders, malignancies, or the use of certain medications that affect von Willebrand factor levels.