Idiopathic hypereosinophilic syndrome [IHES]
ICD-10 D72.110 is a billable code used to indicate a diagnosis of idiopathic hypereosinophilic syndrome [ihes].
Idiopathic hypereosinophilic syndrome (IHES) is a rare hematological disorder characterized by persistently elevated eosinophil counts in the absence of identifiable causes. Eosinophils are a type of white blood cell involved in the body's immune response, particularly in allergic reactions and parasitic infections. In IHES, the eosinophilia can lead to significant tissue damage and organ dysfunction due to the infiltration of eosinophils into various tissues. Commonly affected organs include the skin, lungs, heart, and gastrointestinal tract. Patients may present with symptoms such as fever, weight loss, fatigue, and organ-specific symptoms depending on the sites of eosinophilic infiltration. The diagnosis is primarily clinical, supported by laboratory findings of eosinophilia and exclusion of secondary causes such as infections, malignancies, and autoimmune diseases. Management often involves corticosteroids and other immunosuppressive therapies to control eosinophil levels and mitigate organ damage. Due to the complexity of the condition and its potential overlap with other white blood cell disorders, accurate coding is essential for appropriate treatment and reimbursement.
Complete blood count (CBC) with differential, detailed patient history, and clinical findings.
Patients presenting with unexplained eosinophilia and associated symptoms.
Ensure all laboratory results are documented and correlate with clinical findings.
Immunological workup to rule out allergic or autoimmune conditions.
Patients with recurrent infections or allergic symptoms alongside eosinophilia.
Document any immunodeficiencies that may coexist with IHES.
Used to confirm eosinophilia in suspected IHES cases.
Document the eosinophil count and any relevant clinical findings.
Hematology specialists should ensure comprehensive lab results are included.
Common symptoms include fatigue, fever, weight loss, and organ-specific symptoms such as respiratory issues, skin rashes, and gastrointestinal disturbances.
Diagnosis is based on clinical evaluation, laboratory findings showing eosinophilia, and exclusion of secondary causes through comprehensive testing.
