Nelson's syndrome
ICD-10 E24.1 is a billable code used to indicate a diagnosis of nelson's syndrome.
Nelson's syndrome is a rare endocrine disorder that occurs in patients who have undergone bilateral adrenalectomy, typically for the treatment of Cushing's disease. The removal of the adrenal glands leads to a significant decrease in cortisol production, which in turn causes an increase in adrenocorticotropic hormone (ACTH) secretion from the pituitary gland due to loss of negative feedback. This hypersecretion of ACTH can result in the enlargement of the pituitary gland, leading to pituitary adenomas. Clinically, patients may present with symptoms related to excess ACTH, such as hyperpigmentation of the skin, fatigue, and other hormonal imbalances. The condition is characterized by the presence of a pituitary tumor, which can cause additional complications, including headaches and visual disturbances. Management often involves monitoring hormone levels and may require surgical intervention if the pituitary adenoma becomes symptomatic or grows significantly. Understanding the interplay between the adrenal, pituitary, and parathyroid glands is crucial in diagnosing and managing this syndrome effectively.
Thorough documentation of hormone levels, imaging studies, and patient symptoms.
Patients presenting with symptoms of adrenal insufficiency or pituitary adenomas.
Endocrinologists must ensure accurate tracking of hormone replacement therapy and its effects.
Detailed operative reports and post-operative follow-up notes.
Surgical intervention for pituitary adenomas causing visual disturbances.
Neurosurgeons should document the extent of tumor resection and any complications.
Used when a patient with Nelson's syndrome requires surgical intervention for a pituitary adenoma.
Operative report detailing the procedure and findings.
Neurosurgeons must document the extent of resection and any complications.
Common symptoms include fatigue, hyperpigmentation, and symptoms related to pituitary adenomas such as headaches and visual disturbances.
Diagnosis is based on clinical symptoms, elevated ACTH levels, and imaging studies showing pituitary enlargement.
