Other childhood disintegrative disorder
ICD-10 F84.3 is a billable code used to indicate a diagnosis of other childhood disintegrative disorder.
Other childhood disintegrative disorder, also known as Heller's syndrome, is a rare neurodevelopmental disorder characterized by a significant regression in multiple areas of functioning after at least two years of normal development. This condition typically manifests in children between the ages of 2 and 4 years, where they may lose previously acquired skills in language, social interaction, and motor abilities. Unlike autism spectrum disorders, children with disintegrative disorder experience a more profound and rapid decline in functioning. Symptoms may include a loss of social engagement, communication skills, and the ability to perform daily activities. The etiology of this disorder is not well understood, but it is believed to involve a combination of genetic and environmental factors. Diagnosis is primarily clinical, based on observed developmental regression and the exclusion of other conditions. Early intervention is crucial for improving outcomes, and treatment often involves a multidisciplinary approach, including behavioral therapy, speech therapy, and educational support.
Detailed developmental history, including milestones and regression timeline.
Assessment of a child presenting with sudden loss of language and social skills.
Need for collaboration with speech and occupational therapists for comprehensive evaluation.
Psychiatric evaluation notes detailing behavioral changes and regression.
Evaluation of a child with behavioral issues and loss of previously acquired skills.
Consideration of comorbid mental health conditions that may complicate diagnosis.
Used during initial assessments of children suspected of having developmental disorders.
Documentation of the screening results and any follow-up recommendations.
Pediatricians should ensure comprehensive developmental history is included.
Key symptoms include significant regression in language, social skills, and motor abilities after a period of normal development, typically observed between ages 2 and 4.
Diagnosis is primarily clinical, based on observed developmental regression and the exclusion of other neurodevelopmental disorders. A thorough developmental history and assessment are essential.
