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ICD-10 Guide
ICD-10 CodesG04.00

G04.00

Billable

Acute disseminated encephalitis and encephalomyelitis, unspecified

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/05/2025

Code Description

ICD-10 G04.00 is a billable code used to indicate a diagnosis of acute disseminated encephalitis and encephalomyelitis, unspecified.

Key Diagnostic Point:

Acute disseminated encephalitis and encephalomyelitis (ADEM) is a rare neurological condition characterized by widespread inflammation of the brain and spinal cord. It often follows a viral infection, such as measles, mumps, or influenza, and can occur after vaccination. The condition is marked by symptoms such as fever, headache, confusion, seizures, and neurological deficits. Diagnosis typically involves MRI imaging, which may show lesions in the brain and spinal cord, and lumbar puncture to analyze cerebrospinal fluid (CSF) for inflammatory markers. Treatment usually includes corticosteroids to reduce inflammation and supportive care. The unspecified designation indicates that the specific cause of the encephalitis or encephalomyelitis has not been determined, which can complicate management and coding. Clinicians must be vigilant in monitoring for potential complications, including seizures and long-term neurological deficits.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Unspecified nature of the condition complicates coding accuracy.
  • Differentiation from other CNS infections requires thorough documentation.
  • Potential overlap with other encephalitis codes increases complexity.
  • Need for precise clinical details to support the diagnosis.

Audit Risk Factors

  • Insufficient documentation of clinical findings.
  • Failure to specify the cause of encephalitis.
  • Inconsistent use of terminology in clinical notes.
  • Lack of supporting imaging or lab results.

Specialty Focus

Medical Specialties

Neurology

Documentation Requirements

Detailed neurological examination findings, imaging results, and treatment plans.

Common Clinical Scenarios

Patients presenting with acute neurological symptoms following a viral illness.

Billing Considerations

Ensure clarity in documentation regarding the onset and progression of symptoms.

Infectious Disease

Documentation Requirements

History of recent infections, vaccination status, and laboratory results.

Common Clinical Scenarios

Patients with encephalitis following viral infections or vaccinations.

Billing Considerations

Document any infectious agents identified to support coding.

Coding Guidelines

Inclusion Criteria

Use G04.00 When
  • According to ICD
  • 10 guidelines, G04
  • 00 should be used when the specific cause of the encephalitis or encephalomyelitis is not documented
  • Coders should ensure that the clinical documentation supports the diagnosis and that other potential causes are ruled out

Exclusion Criteria

Do NOT use G04.00 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

70450CPT Code

CT scan of the head

Clinical Scenario

Used to evaluate for acute changes in patients with suspected encephalitis.

Documentation Requirements

Document indications for imaging and findings.

Specialty Considerations

Neurology specialists should ensure imaging correlates with clinical findings.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of encephalitis and encephalomyelitis, improving data accuracy and facilitating better patient management. G04.00 serves as a catch-all for unspecified cases, which can lead to increased scrutiny during audits.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of encephalitis and encephalomyelitis, improving data accuracy and facilitating better patient management. G04.00 serves as a catch-all for unspecified cases, which can lead to increased scrutiny during audits.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for more specific coding of encephalitis and encephalomyelitis, improving data accuracy and facilitating better patient management. G04.00 serves as a catch-all for unspecified cases, which can lead to increased scrutiny during audits.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What is the difference between G04.00 and G04.01?

G04.00 is used when the cause of the encephalitis is unspecified, while G04.01 is used when a specific viral cause is identified.