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v1.0.0
ICD-10 Guide
ICD-10 CodesG90.0

G90.0

Billable

Idiopathic peripheral autonomic neuropathy

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/05/2025

Code Description

ICD-10 G90.0 is a billable code used to indicate a diagnosis of idiopathic peripheral autonomic neuropathy.

Key Diagnostic Point:

Idiopathic peripheral autonomic neuropathy (IPAN) is a condition characterized by dysfunction of the autonomic nervous system without a known cause. This disorder affects the peripheral nerves that control involuntary bodily functions, including heart rate, blood pressure, digestion, and temperature regulation. Patients may experience a range of symptoms such as orthostatic hypotension, gastrointestinal disturbances, and abnormal sweating. The idiopathic nature of the condition means that it cannot be attributed to other identifiable diseases or conditions, making diagnosis challenging. The pathophysiology of IPAN is not well understood, but it is believed to involve autoimmune mechanisms or small fiber neuropathy. Diagnosis typically involves a thorough clinical evaluation, including a detailed history and physical examination, alongside autonomic testing. Management focuses on symptomatic relief and may include medications to address specific symptoms, lifestyle modifications, and physical therapy. Due to its complex nature and the variability in patient presentation, coding for IPAN requires careful consideration of the clinical context and associated symptoms.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in symptom presentation among patients
  • Need for comprehensive documentation to support diagnosis
  • Potential overlap with other neuropathic conditions
  • Lack of definitive diagnostic tests for idiopathic cases

Audit Risk Factors

  • Insufficient documentation of symptoms and clinical findings
  • Inconsistent use of the code across different providers
  • Failure to document the idiopathic nature of the condition
  • Lack of follow-up documentation to support ongoing treatment

Specialty Focus

Medical Specialties

Neurology

Documentation Requirements

Detailed neurological examination findings, autonomic testing results, and symptom history.

Common Clinical Scenarios

Patients presenting with unexplained dizziness, syncope, or gastrointestinal issues.

Billing Considerations

Ensure that the idiopathic nature is clearly documented to avoid misclassification.

Internal Medicine

Documentation Requirements

Comprehensive medical history, including any comorbid conditions that may affect autonomic function.

Common Clinical Scenarios

Patients with multiple symptoms affecting various organ systems without a clear diagnosis.

Billing Considerations

Documenting the exclusion of other potential causes is crucial for accurate coding.

Coding Guidelines

Inclusion Criteria

Use G90.0 When
  • According to ICD
  • 10 guidelines, G90
  • 0 should be used when the condition is confirmed as idiopathic and other causes have been ruled out
  • Documentation must support the diagnosis, including symptomatology and any relevant tests performed

Exclusion Criteria

Do NOT use G90.0 When
  • Exclusion criteria include known causes of autonomic neuropathy

Related ICD-10 Codes

Related CPT Codes

95921CPT Code

Nerve conduction studies

Clinical Scenario

Used to evaluate nerve function in patients suspected of having neuropathy.

Documentation Requirements

Results of nerve conduction studies must be documented, including any abnormalities found.

Specialty Considerations

Neurologists should ensure that the rationale for testing is clearly stated.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of idiopathic conditions, improving the ability to track and manage autonomic neuropathies. G90.0 provides a clear designation for idiopathic cases, which aids in research and treatment planning.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of idiopathic conditions, improving the ability to track and manage autonomic neuropathies. G90.0 provides a clear designation for idiopathic cases, which aids in research and treatment planning.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for more specific coding of idiopathic conditions, improving the ability to track and manage autonomic neuropathies. G90.0 provides a clear designation for idiopathic cases, which aids in research and treatment planning.

Resources

Clinical References

  • •
    American Academy of Neurology

Coding & Billing References

  • •
    American Academy of Neurology

Frequently Asked Questions

What is the primary symptom of idiopathic peripheral autonomic neuropathy?

The primary symptoms can vary widely but often include dizziness, fainting, gastrointestinal issues, and abnormal sweating.

How is idiopathic peripheral autonomic neuropathy diagnosed?

Diagnosis typically involves a thorough clinical evaluation, autonomic function tests, and ruling out other potential causes of autonomic dysfunction.