Primary pulmonary hypertension
ICD-10 I27.0 is a billable code used to indicate a diagnosis of primary pulmonary hypertension.
Primary pulmonary hypertension (PPH) is a rare and progressive disorder characterized by elevated blood pressure in the pulmonary arteries, leading to right heart failure and decreased exercise tolerance. Clinically, patients may present with symptoms such as dyspnea on exertion, fatigue, chest pain, and syncope. The anatomy involved includes the pulmonary arteries, which transport blood from the heart to the lungs for oxygenation. Over time, the increased pressure can lead to vascular remodeling, resulting in further complications such as right ventricular hypertrophy and eventual heart failure. Diagnosis typically involves echocardiography, right heart catheterization, and pulmonary function tests to assess the severity of the condition. Differential diagnoses must be considered, including secondary causes of pulmonary hypertension, such as left heart disease, chronic lung disease, or thromboembolic disease. Accurate diagnosis is crucial for appropriate management and treatment options, which may include medications, lifestyle changes, and in severe cases, lung transplantation.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
I27.0 specifically covers primary pulmonary hypertension, which is idiopathic in nature and not attributable to other underlying conditions. It is characterized by elevated mean pulmonary arterial pressure without a known cause.
I27.0 should be used when the pulmonary hypertension is confirmed to be primary and not secondary to other conditions such as left heart disease or chronic lung disease. Proper diagnostic criteria must be met.
Documentation should include clinical findings, results from echocardiography or right heart catheterization, and any relevant history that rules out secondary causes of pulmonary hypertension.
