Alveolar proteinosis
ICD-10 J84.01 is a billable code used to indicate a diagnosis of alveolar proteinosis.
Alveolar proteinosis is a rare lung disease characterized by the accumulation of surfactant proteins and lipids within the alveoli, leading to impaired gas exchange and respiratory distress. Clinically, patients may present with symptoms such as progressive dyspnea, cough, and fatigue. The disease primarily affects the lungs, where the alveoli, the tiny air sacs responsible for gas exchange, become filled with a proteinaceous material. This accumulation can result from various causes, including autoimmune disorders, exposure to certain environmental factors, or may be idiopathic in nature. Disease progression can vary, with some patients experiencing acute exacerbations while others may have a more chronic course. Diagnosis typically involves imaging studies such as chest CT scans, which reveal characteristic ground-glass opacities, and bronchoalveolar lavage, where the presence of excess surfactant can be confirmed. Early recognition and management are crucial to prevent complications such as respiratory failure.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
J84.01 specifically covers idiopathic pulmonary alveolar proteinosis, which is characterized by the accumulation of surfactant in the alveoli. It does not include secondary forms of alveolar proteinosis caused by other underlying conditions.
J84.01 should be used when the diagnosis of idiopathic pulmonary alveolar proteinosis is confirmed through clinical evaluation and diagnostic imaging. It should not be used for secondary forms of alveolar proteinosis, which may require different coding.
Documentation for J84.01 should include clinical findings, imaging results showing characteristic patterns, and results from bronchoalveolar lavage that confirm the diagnosis of alveolar proteinosis.
