Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
ICD-10 J84.178 is a billable code used to indicate a diagnosis of other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere.
J84.178 refers to other interstitial pulmonary diseases with fibrosis that are classified elsewhere. This category encompasses a variety of lung conditions characterized by the accumulation of fibrous tissue within the lung interstitium, which can lead to progressive respiratory dysfunction. Common clinical presentations include dyspnea (shortness of breath), chronic cough, and fatigue. The anatomy involved primarily includes the alveoli and interstitial spaces of the lungs, where inflammation and fibrosis can disrupt normal gas exchange. Disease progression can vary significantly, with some patients experiencing rapid deterioration while others may have a more indolent course. Diagnostic considerations include high-resolution computed tomography (HRCT) scans, pulmonary function tests, and sometimes lung biopsy to confirm the presence of fibrosis and rule out other conditions. It is crucial to differentiate J84.178 from other interstitial lung diseases, as the underlying etiology may influence management and prognosis.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
J84.178 encompasses various interstitial lung diseases with fibrosis that are not classified elsewhere, including conditions like sarcoidosis with pulmonary involvement, hypersensitivity pneumonitis, and fibrosis associated with systemic diseases such as lupus or scleroderma.
J84.178 should be used when the interstitial pulmonary disease with fibrosis does not fit into more specific categories, such as idiopathic pulmonary fibrosis (J84.1) or other defined interstitial lung diseases. It is essential to ensure that the documentation supports the diagnosis of fibrosis in the context of another underlying disease.
Documentation should include a clear diagnosis of interstitial pulmonary disease with fibrosis, results from imaging studies (like HRCT), pulmonary function tests, and any relevant clinical history that indicates the underlying condition contributing to the fibrosis.
