Adult pulmonary Langerhans cell histiocytosis
ICD-10 J84.82 is a billable code used to indicate a diagnosis of adult pulmonary langerhans cell histiocytosis.
Adult pulmonary Langerhans cell histiocytosis (LCH) is a rare disorder characterized by the proliferation of Langerhans cells, a type of dendritic cell involved in immune response, within the lungs. Clinically, patients may present with respiratory symptoms such as cough, dyspnea, and chest pain, often accompanied by a history of smoking or exposure to environmental toxins. The disease primarily affects the lung parenchyma, leading to the formation of cysts and nodules, which can be identified through imaging studies like CT scans. Disease progression can vary; some patients may experience spontaneous remission, while others may develop chronic respiratory issues or pulmonary fibrosis. Diagnostic considerations include a thorough clinical evaluation, imaging studies, and histopathological confirmation through lung biopsy, which reveals the characteristic Langerhans cells. Given the potential for overlap with other interstitial lung diseases, accurate diagnosis is crucial for appropriate management.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
J84.82 specifically covers adult pulmonary Langerhans cell histiocytosis, which is characterized by the accumulation of Langerhans cells in the lungs, leading to respiratory symptoms and potential lung damage.
J84.82 should be used when the diagnosis is confirmed as adult pulmonary LCH, particularly when histological evidence is available, differentiating it from other interstitial lung diseases or pediatric forms of LCH.
Documentation should include a detailed clinical history, imaging studies (such as CT scans), and histopathological findings from lung biopsies that confirm the presence of Langerhans cells.
