Alveolar capillary dysplasia with vein misalignment
ICD-10 J84.843 is a billable code used to indicate a diagnosis of alveolar capillary dysplasia with vein misalignment.
Alveolar capillary dysplasia with vein misalignment (ACD) is a rare congenital lung disorder characterized by abnormal development of the alveolar capillaries and misalignment of pulmonary veins. Clinically, patients often present with severe respiratory distress shortly after birth, typically requiring immediate respiratory support. The anatomy involved includes the alveoli, which are the tiny air sacs in the lungs where gas exchange occurs, and the pulmonary veins, which transport oxygenated blood from the lungs to the heart. Disease progression can be rapid, with affected infants experiencing hypoxemia and respiratory failure due to inadequate gas exchange. Diagnosis is primarily based on clinical presentation, imaging studies such as chest X-rays or CT scans, and histological examination of lung tissue, which reveals the characteristic capillary dysplasia. Genetic testing may also be considered to identify underlying mutations associated with the condition. Early recognition and intervention are critical to improving outcomes, as the condition can lead to significant morbidity and mortality if not managed promptly.
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
Standard ICD-10-CM documentation requirements apply
Various clinical presentations within this specialty area
Follow specialty-specific billing guidelines
J84.843 specifically covers alveolar capillary dysplasia with vein misalignment, a condition that leads to significant respiratory distress in neonates due to abnormal lung development.
J84.843 should be used when a patient presents with alveolar capillary dysplasia specifically associated with vein misalignment, differentiating it from other forms of dysplasia that do not involve vein misalignment.
Documentation should include clinical findings of respiratory distress, imaging results indicating lung abnormalities, and histopathological evidence of capillary dysplasia and vein misalignment.
