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ICD-10 Guide
ICD-10 CodesChapter 14: Diseases of the genitourinary systemN01

N01

Non-billable

Rapidly progressive nephritic syndrome

Chapter 14:Diseases of the genitourinary system

BILLABLE STATUSNo
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/12/2025

Code Description

ICD-10 N01 is a used to indicate a diagnosis of rapidly progressive nephritic syndrome.

Key Diagnostic Point:

Rapidly progressive nephritic syndrome (N01) is a clinical condition characterized by a rapid decline in kidney function, often leading to acute kidney injury. This syndrome is typically associated with various underlying causes, including autoimmune diseases, infections, and certain medications. The condition is marked by the presence of glomerular inflammation and can lead to significant morbidity if not promptly diagnosed and treated. Clinicians must be vigilant in identifying the signs and symptoms, which may include hematuria, proteinuria, and elevated blood pressure, as early intervention is crucial for improving patient outcomes.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

    Audit Risk Factors

      Specialty Focus

      Medical Specialties

      Nephrology

      Documentation Requirements

      Detailed history of kidney function, laboratory results including creatinine and protein levels, and imaging studies if applicable.

      Common Clinical Scenarios

      Evaluation of patients presenting with acute kidney injury, glomerulonephritis, or nephritic syndrome symptoms.

      Billing Considerations

      Ensure accurate documentation of underlying causes and comorbidities that may contribute to rapidly progressive nephritic syndrome.

      Internal Medicine

      Documentation Requirements

      Complete patient history, physical examination findings, and results from relevant laboratory tests.

      Common Clinical Scenarios

      Management of patients with systemic symptoms indicating a possible nephritic syndrome and concurrent medical conditions.

      Billing Considerations

      Documenting the progression of symptoms and treatment responses is critical for ongoing management and coding.

      Emergency Medicine

      Documentation Requirements

      Rapid assessment notes, vital signs, laboratory results, and treatment interventions.

      Common Clinical Scenarios

      Initial evaluation of patients presenting with acute symptoms of nephritic syndrome, such as hematuria or hypertension.

      Billing Considerations

      Document the urgency of care and any immediate interventions performed to stabilize kidney function.

      Urology

      Documentation Requirements

      Urological assessment, imaging studies, and history of urinary tract symptoms.

      Common Clinical Scenarios

      Referral of patients with urinary complications stemming from nephritic syndrome or associated urological disorders.

      Billing Considerations

      Accurate coding for any surgical interventions or diagnostic procedures performed in relation to nephritic conditions.

      Related CPT Codes

      74176CPT Code

      Clinical Scenario

      Documentation Requirements

      Indication for the ultrasound, findings of the abdominal examination, and any relevant laboratory data.

      82043CPT Code

      Clinical Scenario

      Documentation Requirements

      Clear indication of the reason for testing and previous lab results for comparison.

      84450CPT Code

      Clinical Scenario

      Documentation Requirements

      Document the clinical context justifying the test and previous creatinine levels if available.

      99284CPT Code

      Clinical Scenario

      Documentation Requirements

      Detailed account of presenting symptoms, examination findings, and interventions performed.

      93000CPT Code

      Clinical Scenario

      Documentation Requirements

      Clinical rationale for ECG, including symptoms of chest pain or arrhythmias.

      ICD-10 Impact

      Diagnostic & Documentation Impact

      Enhanced Specificity

      ICD-10 Improvements

      The clinical and administrative impact of the N01 code category is significant, as it plays a crucial role in quality measures related to kidney health and management of acute kidney injury. Accurate coding can influence population health initiatives aimed at reducing the incidence of kidney disease and improving patient outcomes. Furthermore, as healthcare trends shift towards value-based care, proper documentation and coding of rapidly progressive nephritic syndrome can affect reimbursement rates and overall healthcare costs.

      ICD-9 vs ICD-10

      The clinical and administrative impact of the N01 code category is significant, as it plays a crucial role in quality measures related to kidney health and management of acute kidney injury. Accurate coding can influence population health initiatives aimed at reducing the incidence of kidney disease and improving patient outcomes. Furthermore, as healthcare trends shift towards value-based care, proper documentation and coding of rapidly progressive nephritic syndrome can affect reimbursement rates and overall healthcare costs.

      Reimbursement & Billing Impact

      reimbursement rates and overall healthcare costs.

      Resources

      Clinical References

      • •
        Kidney Disease: Improving Global Outcomes (KDIGO)
      • •
        American Society of Nephrology (ASN)
      • •
        National Kidney Foundation (NKF)
      • •
        UpToDate Nephrology Section

      Coding & Billing References

      • •
        Kidney Disease: Improving Global Outcomes (KDIGO)
      • •
        American Society of Nephrology (ASN)
      • •
        National Kidney Foundation (NKF)
      • •
        UpToDate Nephrology Section

      Frequently Asked Questions

      What conditions are included in N01?

      N01 encompasses rapidly progressive nephritic syndrome due to various etiologies, including but not limited to, anti-glomerular basement membrane disease, vasculitis, and post-infectious glomerulonephritis.

      When should I use N01 codes?

      N01 codes should be used when a patient presents with symptoms indicative of rapidly progressive nephritic syndrome, particularly when there is evidence of acute kidney injury and glomerular inflammation.

      What documentation is required for N01?

      Documentation should include a detailed clinical history, laboratory findings, imaging studies, and any relevant diagnostic procedures that support the diagnosis of rapidly progressive nephritic syndrome.