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v1.0.0
ICD-10 Guide
ICD-10 CodesN01.0

N01.0

Billable

Rapidly progressive nephritic syndrome with minor glomerular abnormality

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/18/2025

Code Description

ICD-10 N01.0 is a billable code used to indicate a diagnosis of rapidly progressive nephritic syndrome with minor glomerular abnormality.

Key Diagnostic Point:

Rapidly progressive nephritic syndrome (RPNS) is characterized by a swift decline in renal function, often leading to end-stage renal disease within weeks to months. This syndrome is typically associated with significant proteinuria, hematuria, and varying degrees of renal impairment. The minor glomerular abnormalities observed in RPNS may include minimal changes or mild mesangial proliferation, which can be detected through renal biopsy. Clinically, patients may present with symptoms such as edema, hypertension, and signs of renal failure. The pathophysiology often involves an autoimmune process or systemic disease, leading to glomerular inflammation and damage. Early diagnosis and management are crucial to prevent irreversible kidney damage, and treatment may include corticosteroids, immunosuppressants, and supportive care. Monitoring renal function and protein levels is essential in managing this condition effectively.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in clinical presentation and underlying causes
  • Need for precise documentation of renal biopsy findings
  • Differentiation from other nephritic syndromes
  • Potential overlap with nephrotic syndrome

Audit Risk Factors

  • Inadequate documentation of renal biopsy findings
  • Failure to specify the degree of proteinuria and hematuria
  • Misclassification of the syndrome type
  • Lack of follow-up documentation on renal function

Specialty Focus

Medical Specialties

Nephrology

Documentation Requirements

Detailed clinical notes on renal function, laboratory results, and biopsy findings.

Common Clinical Scenarios

Patients presenting with acute kidney injury, unexplained hematuria, or significant proteinuria.

Billing Considerations

Ensure accurate staging of renal impairment and documentation of treatment response.

Pathology

Documentation Requirements

Comprehensive reports on renal biopsy histology and immunofluorescence findings.

Common Clinical Scenarios

Biopsy evaluations for patients with suspected glomerular diseases.

Billing Considerations

Clear communication of findings to nephrologists for appropriate coding.

Coding Guidelines

Inclusion Criteria

Use N01.0 When
  • Follow the official ICD
  • CM coding guidelines, ensuring accurate documentation of clinical findings, laboratory results, and treatment plans
  • Include specific details about the renal biopsy and any associated conditions

Exclusion Criteria

Do NOT use N01.0 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

88172CPT Code

Renal biopsy, percutaneous

Clinical Scenario

Used when a renal biopsy is performed to confirm diagnosis.

Documentation Requirements

Document indication for biopsy, findings, and any complications.

Specialty Considerations

Nephrologists must ensure proper coding based on biopsy results.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of nephritic syndromes, improving the accuracy of data collection and reimbursement processes. N01.0 provides a clear distinction from other nephritic and nephrotic conditions.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of nephritic syndromes, improving the accuracy of data collection and reimbursement processes. N01.0 provides a clear distinction from other nephritic and nephrotic conditions.

Reimbursement & Billing Impact

reimbursement processes. N01.0 provides a clear distinction from other nephritic and nephrotic conditions.

Resources

Clinical References

  • •
    American Academy of Nephrology

Coding & Billing References

  • •
    American Academy of Nephrology

Frequently Asked Questions

What are the key symptoms of rapidly progressive nephritic syndrome?

Key symptoms include hematuria, proteinuria, edema, hypertension, and signs of acute kidney injury.

How is rapidly progressive nephritic syndrome diagnosed?

Diagnosis typically involves clinical evaluation, laboratory tests for proteinuria and hematuria, and confirmation through renal biopsy.