Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
ICD-10 N01.1 is a billable code used to indicate a diagnosis of rapidly progressive nephritic syndrome with focal and segmental glomerular lesions.
Rapidly progressive nephritic syndrome (RPNS) is characterized by a swift decline in renal function, often leading to end-stage renal disease within weeks to months. This condition is associated with focal and segmental glomerular lesions, which are identified through renal biopsy. Clinically, patients present with symptoms of nephritis, including hematuria (blood in urine), proteinuria (excess protein in urine), and hypertension. The pathophysiology involves an inflammatory response that damages the glomeruli, leading to a rapid decrease in glomerular filtration rate (GFR). Diagnosis typically requires a renal biopsy to confirm the presence of specific glomerular lesions, such as crescent formation, which is indicative of severe glomerular injury. Management of RPNS often involves immunosuppressive therapy, including corticosteroids and other agents, to reduce inflammation and prevent further renal damage. Close monitoring of renal function and regular follow-up with nephrology specialists are essential for optimal patient outcomes.
Detailed clinical notes, renal function tests, biopsy results, and treatment plans.
Patients presenting with acute renal failure, hematuria, and proteinuria.
Ensure clarity in documenting the type of glomerular lesions and the patient's response to treatment.
Comprehensive pathology reports detailing biopsy findings.
Evaluation of renal biopsies for glomerular diseases.
Accurate description of histological findings is crucial for correct coding.
Used when a renal biopsy is performed to confirm diagnosis.
Pathology report and clinical notes supporting the need for biopsy.
Nephrologists must document the rationale for biopsy in the context of rapidly progressive symptoms.
Key symptoms include hematuria, proteinuria, hypertension, and rapid decline in renal function.
Diagnosis typically involves clinical evaluation, laboratory tests showing proteinuria and hematuria, and confirmation through renal biopsy.
Treatment often includes immunosuppressive therapy, such as corticosteroids, and management of associated conditions like hypertension.
