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ICD-10 Guide
ICD-10 CodesN01.9

N01.9

Billable

Rapidly progressive nephritic syndrome with unspecified morphologic changes

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/18/2025

Code Description

ICD-10 N01.9 is a billable code used to indicate a diagnosis of rapidly progressive nephritic syndrome with unspecified morphologic changes.

Key Diagnostic Point:

Rapidly progressive nephritic syndrome (RPNS) is characterized by a rapid decline in renal function, typically defined as a decrease in glomerular filtration rate (GFR) of more than 50% within a short period, often days to weeks. This syndrome is associated with significant clinical features such as hematuria, proteinuria, and hypertension. The morphologic changes in RPNS can vary widely, often necessitating renal biopsy for definitive diagnosis. Common underlying causes include autoimmune diseases, infections, and certain medications. Patients may present with symptoms such as edema, fatigue, and oliguria. The management of RPNS involves addressing the underlying cause, which may include immunosuppressive therapy, corticosteroids, or plasmapheresis, depending on the etiology. Close monitoring of renal function and laboratory parameters is essential to guide treatment and assess response.

Code Complexity Analysis

Complexity Rating: High

High Complexity

Complexity Factors

  • Variety of underlying causes leading to RPNS
  • Need for renal biopsy to determine specific morphologic changes
  • Differential diagnosis with other nephritic syndromes
  • Potential for rapid clinical deterioration requiring urgent intervention

Audit Risk Factors

  • Inadequate documentation of clinical findings
  • Failure to specify underlying causes or contributing factors
  • Lack of renal biopsy results in the medical record
  • Inconsistent coding of associated symptoms like hematuria and proteinuria

Specialty Focus

Medical Specialties

Nephrology

Documentation Requirements

Detailed clinical notes including symptoms, lab results, and treatment plans.

Common Clinical Scenarios

Patients presenting with acute kidney injury, hematuria, and proteinuria.

Billing Considerations

Ensure renal biopsy results are documented and correlate with clinical findings.

Internal Medicine

Documentation Requirements

Comprehensive history and physical examination, including review of systems.

Common Clinical Scenarios

Management of patients with systemic diseases leading to nephritis.

Billing Considerations

Document any systemic symptoms that may indicate an underlying cause.

Coding Guidelines

Inclusion Criteria

Use N01.9 When
  • Follow official ICD
  • CM guidelines for coding nephritic syndrome, ensuring to document the clinical presentation, diagnostic tests, and treatment plans
  • Include any relevant laboratory findings such as creatinine levels and urinalysis results

Exclusion Criteria

Do NOT use N01.9 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

Renal biopsy CPT codeCPT Code

Renal biopsy

Clinical Scenario

Used when a renal biopsy is performed to determine the cause of RPNS.

Documentation Requirements

Document indication for biopsy, consent, and results.

Specialty Considerations

Nephrology specialists should ensure biopsy results are clearly linked to the diagnosis.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of nephritic syndromes, improving the ability to capture the complexity of conditions like RPNS. This specificity aids in better patient management and resource allocation.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of nephritic syndromes, improving the ability to capture the complexity of conditions like RPNS. This specificity aids in better patient management and resource allocation.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for more specific coding of nephritic syndromes, improving the ability to capture the complexity of conditions like RPNS. This specificity aids in better patient management and resource allocation.

Resources

Clinical References

  • •
    American Academy of Nephrology

Coding & Billing References

  • •
    American Academy of Nephrology

Frequently Asked Questions

What are the common causes of rapidly progressive nephritic syndrome?

Common causes include autoimmune diseases (like lupus), infections (such as post-streptococcal glomerulonephritis), and certain medications. Identifying the underlying cause is crucial for effective management.