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ICD-10 Guide
ICD-10 CodesN07.6

N07.6

Billable

Hereditary nephropathy, not elsewhere classified with dense deposit disease

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/18/2025

Code Description

ICD-10 N07.6 is a billable code used to indicate a diagnosis of hereditary nephropathy, not elsewhere classified with dense deposit disease.

Key Diagnostic Point:

N07.6 refers to hereditary nephropathy characterized by dense deposit disease, a specific type of glomerular disorder. This condition is often associated with isolated proteinuria, which is the presence of excess protein in the urine without significant hematuria or other renal symptoms. Dense deposit disease is a rare form of membranoproliferative glomerulonephritis, primarily caused by genetic mutations affecting the complement system, leading to abnormal deposition of complement components in the glomeruli. Patients may present with varying degrees of renal impairment, and the condition can progress to end-stage renal disease. Genetic testing is crucial for diagnosis and management, as it can identify specific mutations linked to hereditary nephropathy. Clinicians must differentiate this condition from other glomerular disorders classified elsewhere, ensuring accurate coding and treatment planning.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Requires understanding of genetic components and hereditary patterns.
  • Differentiation from other nephropathies and glomerular disorders.
  • Need for precise documentation of proteinuria levels and renal function.
  • Involves interpretation of genetic testing results.

Audit Risk Factors

  • Inadequate documentation of genetic testing results.
  • Failure to specify the type of proteinuria present.
  • Misclassification of hereditary nephropathy as acquired conditions.
  • Lack of detailed clinical notes regarding patient history.

Specialty Focus

Medical Specialties

Nephrology

Documentation Requirements

Detailed clinical notes on renal function, proteinuria levels, and genetic testing results.

Common Clinical Scenarios

Patients presenting with isolated proteinuria and family history of kidney disease.

Billing Considerations

Ensure comprehensive documentation of all renal assessments and laboratory results.

Genetics

Documentation Requirements

Records of genetic testing and family history of hereditary nephropathy.

Common Clinical Scenarios

Patients undergoing evaluation for hereditary kidney disorders.

Billing Considerations

Documentation must include the rationale for genetic testing and results interpretation.

Coding Guidelines

Inclusion Criteria

Use N07.6 When
  • According to ICD
  • 10 guidelines, N07
  • 6 should be used when the condition is specifically identified as hereditary nephropathy with dense deposit disease
  • Coders must ensure that the diagnosis is supported by clinical documentation and that other potential causes of nephropathy are ruled out

Exclusion Criteria

Do NOT use N07.6 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

81228CPT Code

Genetic testing for complement component mutations

Clinical Scenario

Used when hereditary nephropathy is suspected based on family history.

Documentation Requirements

Documentation of clinical indications for genetic testing and results.

Specialty Considerations

Nephrology specialists should ensure that genetic testing is clearly linked to the diagnosis.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of hereditary nephropathies, improving the accuracy of data collection and reimbursement processes. N07.6 provides a distinct code for dense deposit disease, facilitating better tracking of this rare condition.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of hereditary nephropathies, improving the accuracy of data collection and reimbursement processes. N07.6 provides a distinct code for dense deposit disease, facilitating better tracking of this rare condition.

Reimbursement & Billing Impact

reimbursement processes. N07.6 provides a distinct code for dense deposit disease, facilitating better tracking of this rare condition.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What is the significance of genetic testing in N07.6?

Genetic testing is crucial for confirming the diagnosis of hereditary nephropathy with dense deposit disease, as it identifies specific mutations that can guide treatment and management strategies.