Double outlet right ventricle
ICD-10 Q20.1 is a billable code used to indicate a diagnosis of double outlet right ventricle.
Double outlet right ventricle (DORV) is a congenital heart defect characterized by both the aorta and pulmonary artery arising from the right ventricle, rather than the normal configuration where the aorta arises from the left ventricle. This condition can lead to significant hemodynamic abnormalities, as the systemic and pulmonary circulations are not properly separated. DORV may present with various associated anomalies, including ventricular septal defects (VSDs) and other structural heart defects. The clinical presentation can vary widely, from asymptomatic cases detected incidentally to severe cyanosis and heart failure in neonates. Diagnosis typically involves echocardiography, which provides visualization of the heart's structure and blood flow. Management often requires surgical intervention to correct the anatomical defects and improve blood flow, with the timing of surgery being critical for optimal outcomes. Long-term follow-up is essential due to the risk of complications such as arrhythmias and heart failure as the child grows.
Detailed clinical notes including symptoms, diagnostic imaging results, and treatment plans.
Neonates presenting with cyanosis, failure to thrive, or heart murmurs.
Consideration of growth and development impacts due to congenital heart defects.
Genetic testing results, family history of congenital heart defects, and syndromic associations.
Cases where DORV is part of a genetic syndrome, such as DiGeorge syndrome.
Understanding the genetic implications and counseling families regarding recurrence risks.
Used during surgical intervention for DORV.
Operative report detailing the surgical procedure and any associated anomalies.
Pediatric cardiology and cardiac surgery documentation must be precise.
Common associated anomalies include ventricular septal defects, pulmonary stenosis, and aortic arch anomalies. These can complicate the clinical picture and require careful documentation and management.
