Double inlet ventricle
ICD-10 Q20.4 is a billable code used to indicate a diagnosis of double inlet ventricle.
Double inlet ventricle (DIV) is a complex congenital heart defect characterized by the presence of two atrioventricular valves that connect to a single ventricle. This condition results in a heart that has only one functional ventricle, which can lead to significant hemodynamic challenges. In DIV, both atria empty into the same ventricle, which may be either left or right, while the other ventricle is underdeveloped or absent. This anomaly can be associated with other congenital heart defects, such as ventricular septal defects (VSD), atrial septal defects (ASD), and outflow tract obstructions. The clinical presentation often includes cyanosis, heart failure, and poor growth in infants. Diagnosis typically involves echocardiography, which can visualize the structural abnormalities and assess the function of the heart. Surgical intervention is often required to improve blood flow and oxygenation, and the timing of surgery is critical for optimal outcomes. Long-term follow-up is essential due to the risk of arrhythmias and other complications.
Documentation must include detailed descriptions of the heart's anatomy, associated defects, and the patient's clinical status.
Infants presenting with cyanosis, failure to thrive, and heart murmurs; pre-operative assessments for surgical intervention.
Consideration of growth and developmental milestones in the context of congenital heart disease.
Genetic counseling notes should include family history, potential syndromic associations, and genetic testing results.
Assessment of familial patterns of congenital heart defects; evaluation for syndromes such as Down syndrome or Turner syndrome.
Understanding the genetic basis of congenital heart defects and their implications for family planning.
Used during surgical intervention for double inlet ventricle.
Operative report detailing the surgical procedure and any complications.
Pediatric cardiology should ensure accurate coding of the procedure and any associated congenital anomalies.
The prognosis for children with double inlet ventricle varies based on the presence of associated anomalies and the timing of surgical intervention. With appropriate surgical management, many children can lead active lives, but they require lifelong follow-up due to potential complications.
