ICD-10 Logo
ICDxICD-10 Medical Coding
ICD-10 Logo
ICDxICD-10 Medical Coding
ICD 10 CodesDiagnoses
ICD 10 CodesDiagnoses
ICD-10 Logo
ICDxICD-10 Medical Coding

Comprehensive ICD-10-CM code reference with AI-powered search capabilities.

© 2025 ICD Code Compass. All rights reserved.

Browse

  • All Chapters
  • All Categories
  • Diagnoses

Tools

  • AI Code Search
ICD-10-CM codes are maintained by the CDC and CMS. This tool is for reference purposes only.
v1.0.0
ICD-10 Guide
ICD-10 CodesQ25.49

Q25.49

Billable

Other congenital malformations of aorta

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q25.49 is a billable code used to indicate a diagnosis of other congenital malformations of aorta.

Key Diagnostic Point:

Congenital malformations of the aorta encompass a variety of structural abnormalities that can significantly impact cardiovascular function. These malformations may include conditions such as aortic coarctation, which is characterized by a narrowing of the aorta, leading to increased blood pressure proximal to the defect and decreased blood flow distal to it. Other anomalies may involve abnormal branching patterns or the presence of additional vessels that can complicate normal hemodynamics. Congenital heart defects (CHDs) often coexist with aortic malformations, including septal defects, where there is an abnormal opening between the heart chambers, and tetralogy of Fallot, a complex condition involving four heart defects that can lead to cyanosis and heart failure. Accurate diagnosis typically involves echocardiography, MRI, or CT imaging to visualize the aorta and associated structures. Management may require surgical intervention, particularly in severe cases, to correct the anatomical defects and restore normal blood flow. Early detection and intervention are crucial for improving outcomes in affected pediatric patients.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and severity of aortic malformations
  • Co-occurrence with other congenital heart defects
  • Need for detailed imaging studies for accurate diagnosis
  • Potential for surgical interventions and follow-up coding

Audit Risk Factors

  • Inadequate documentation of the specific type of aortic malformation
  • Failure to capture coexisting congenital heart defects
  • Misclassification of severity or complexity of the condition
  • Lack of clarity in surgical intervention details

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Detailed clinical notes including physical examination findings, imaging results, and treatment plans are essential for accurate coding.

Common Clinical Scenarios

Pediatric patients presenting with symptoms of heart failure, failure to thrive, or cyanosis due to congenital heart defects.

Billing Considerations

Consideration of growth and development milestones in pediatric patients with congenital conditions is crucial for comprehensive care.

Genetics

Documentation Requirements

Genetic testing results, family history, and any syndromic associations should be documented to support the diagnosis of congenital malformations.

Common Clinical Scenarios

Patients with known genetic syndromes presenting with congenital heart defects, requiring genetic counseling and testing.

Billing Considerations

Understanding the genetic basis of congenital malformations can aid in risk assessment and management of affected families.

Coding Guidelines

Inclusion Criteria

Use Q25.49 When
  • Follow the official ICD
  • CM coding guidelines for congenital conditions, ensuring specificity in documentation and adherence to coding conventions for congenital heart defects

Exclusion Criteria

Do NOT use Q25.49 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

33405CPT Code

Repair of coarctation of aorta

Clinical Scenario

Used in cases where surgical intervention is required for aortic coarctation.

Documentation Requirements

Operative reports detailing the procedure and indication for surgery.

Specialty Considerations

Pediatric cardiology may have specific protocols for documenting congenital heart surgeries.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for greater specificity in coding congenital malformations, improving the accuracy of data collection and reimbursement processes.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for greater specificity in coding congenital malformations, improving the accuracy of data collection and reimbursement processes.

Reimbursement & Billing Impact

reimbursement processes.

Resources

Clinical References

  • •
    American Academy of Pediatrics Coding Resources

Coding & Billing References

  • •
    American Academy of Pediatrics Coding Resources

Frequently Asked Questions

What are the common congenital malformations of the aorta?

Common congenital malformations of the aorta include coarctation of the aorta, aortic stenosis, and aortic arch anomalies. These conditions can lead to significant cardiovascular complications and often require surgical intervention.