Congenital pulmonary arteriovenous malformation
ICD-10 Q25.72 is a billable code used to indicate a diagnosis of congenital pulmonary arteriovenous malformation.
Congenital pulmonary arteriovenous malformation (PAVM) is a vascular anomaly characterized by abnormal connections between pulmonary arteries and veins, bypassing the capillary system. This condition can lead to significant clinical complications, including hypoxemia, paradoxical embolism, and pulmonary hypertension. PAVMs can be isolated or part of syndromes such as hereditary hemorrhagic telangiectasia (HHT). Diagnosis is typically made through imaging studies such as chest CT or MRI, which reveal the abnormal vascular connections. Symptoms may include shortness of breath, cyanosis, and recurrent respiratory infections. Management often involves interventional procedures such as embolization to occlude the abnormal vessels, improving oxygenation and reducing the risk of complications. Early detection and treatment are crucial for improving outcomes in affected individuals, particularly in pediatric populations where the impact on growth and development can be significant.
Documentation must include detailed clinical history, physical examination findings, imaging results, and treatment plans. Growth and developmental assessments are also critical.
Common scenarios include a pediatric patient presenting with unexplained hypoxemia or recurrent respiratory infections, necessitating imaging to evaluate for PAVM.
Pediatric patients may present differently than adults, and coders should be aware of age-specific manifestations and treatment protocols.
Genetic counseling notes should document family history, potential syndromic associations, and any genetic testing results.
Scenarios may involve a child with PAVM being evaluated for hereditary hemorrhagic telangiectasia, requiring genetic testing and counseling.
Coders should be aware of the implications of genetic syndromes on coding and the importance of documenting genetic evaluations.
Used in cases where embolization is indicated to treat PAVM.
Documentation must include indications for the procedure, imaging results, and post-procedure outcomes.
Pediatric considerations include age-appropriate sedation and monitoring during the procedure.
Accurate coding for congenital pulmonary arteriovenous malformation is crucial for appropriate management and treatment planning. It also aids in research and understanding the epidemiology of congenital vascular anomalies, ensuring that affected individuals receive the necessary care and interventions.
