Partial anomalous pulmonary venous connection
ICD-10 Q26.3 is a billable code used to indicate a diagnosis of partial anomalous pulmonary venous connection.
Partial anomalous pulmonary venous connection (PAPVC) is a congenital heart defect characterized by the abnormal drainage of one or more pulmonary veins into the right atrium or systemic venous circulation instead of the left atrium. This condition can lead to a range of clinical manifestations, including right heart volume overload, pulmonary hypertension, and potential heart failure if left untreated. PAPVC may occur as an isolated defect or in conjunction with other congenital heart defects, such as atrial septal defects or ventricular septal defects. The severity of symptoms often depends on the number of veins involved and the presence of associated anomalies. Diagnosis typically involves echocardiography, which can visualize the abnormal venous connections, and may be supplemented by cardiac MRI or CT for detailed anatomical assessment. Surgical intervention is often required to correct the anomalous connections, particularly in symptomatic patients, to prevent long-term complications. Early detection and management are crucial for improving outcomes in affected individuals.
Pediatric documentation should include growth parameters, developmental milestones, and specific symptoms related to cardiac function. Detailed family history and prenatal factors may also be relevant.
Common scenarios include infants presenting with respiratory distress, failure to thrive, or cyanosis. Follow-up visits may focus on monitoring growth and cardiac function post-surgery.
Consideration should be given to the age of the patient, as symptoms may vary significantly between neonates and older children.
Genetic documentation should include family history of congenital heart defects, chromosomal abnormalities, and any genetic syndromes associated with PAPVC.
Genetic counseling may be necessary for families with a history of congenital heart defects, especially if there are multiple affected family members.
Consideration of syndromic associations, such as Turner syndrome or Down syndrome, which may increase the risk of congenital heart defects.
Used during surgical intervention for PAPVC correction.
Operative reports must detail the surgical approach and any associated procedures.
Pediatric cardiology specialists should ensure accurate coding of the procedure.
Common symptoms include respiratory distress, cyanosis, and signs of heart failure such as fatigue and poor growth in infants. Symptoms may vary based on the severity of the condition and associated anomalies.
