Portal vein-hepatic artery fistula
ICD-10 Q26.6 is a billable code used to indicate a diagnosis of portal vein-hepatic artery fistula.
Portal vein-hepatic artery fistula is a rare congenital vascular malformation characterized by an abnormal connection between the portal vein and the hepatic artery. This condition can lead to significant hepatic complications due to altered blood flow dynamics, including hepatic ischemia or hyperperfusion. Clinically, patients may present with symptoms such as abdominal pain, jaundice, or signs of liver dysfunction. Diagnosis is typically confirmed through imaging studies such as Doppler ultrasound, CT angiography, or MRI, which can visualize the abnormal vascular connections. Management may involve surgical intervention to correct the fistula, especially in symptomatic patients. Understanding the implications of this condition is crucial for pediatricians and geneticists, as it may be associated with other congenital anomalies or syndromes, necessitating a comprehensive evaluation of the patient’s overall health and genetic background.
Detailed clinical notes on symptoms, imaging results, and treatment plans are essential for pediatric patients with congenital vascular malformations.
Pediatric patients presenting with abdominal pain or jaundice, requiring evaluation for potential vascular anomalies.
Pediatric coders must be aware of the developmental implications of vascular malformations and their potential impact on growth and development.
Genetic evaluations may be necessary to assess for syndromic associations with congenital vascular malformations.
Patients with a family history of congenital anomalies or syndromes undergoing genetic counseling.
Genetic coders should consider the implications of chromosomal abnormalities that may co-occur with vascular malformations.
Used in cases where portal vein-hepatic artery fistula leads to portal hypertension.
Documentation of indications for TIPS and imaging studies supporting the need for the procedure.
Interventional radiology may be involved in the management of these cases.
Common symptoms include abdominal pain, jaundice, and signs of liver dysfunction. Patients may also present with complications related to altered blood flow, such as hepatic ischemia.
