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ICD-10 Guide
ICD-10 CodesQ36.9

Q36.9

Billable

Cleft lip, unilateral

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q36.9 is a billable code used to indicate a diagnosis of cleft lip, unilateral.

Key Diagnostic Point:

Cleft lip, unilateral, is a congenital malformation characterized by a split or opening in the upper lip that occurs on one side. This condition arises during early fetal development when the tissues that form the lip do not fully come together. The severity of the cleft can vary, ranging from a small notch in the lip to a significant gap that extends up into the nose. Unilateral cleft lip can occur in isolation or in conjunction with other congenital anomalies, such as cleft palate. It is essential to assess the impact of this condition on feeding, speech development, and psychosocial aspects as the child grows. Surgical intervention is typically required to repair the cleft, and multidisciplinary care involving pediatricians, surgeons, speech therapists, and genetic counselors is crucial for optimal outcomes. The presence of associated congenital malformations, such as choanal atresia or tracheoesophageal fistula, may complicate the clinical picture and necessitate a comprehensive approach to management.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and severity of cleft lip
  • Potential association with other congenital anomalies
  • Need for multidisciplinary documentation
  • Surgical coding complexities

Audit Risk Factors

  • Inadequate documentation of associated congenital anomalies
  • Failure to capture the severity of the cleft
  • Misalignment with surgical procedure codes
  • Inconsistent coding across different healthcare settings

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Detailed records of feeding difficulties, growth parameters, and developmental milestones are essential. Documentation should also include assessments of psychosocial impacts and referrals to specialists.

Common Clinical Scenarios

Common scenarios include newborns presenting with feeding difficulties due to cleft lip, children requiring speech therapy, and cases where surgical repair is planned.

Billing Considerations

Coders should be aware of the need for comprehensive documentation that captures the multidisciplinary approach to care, including input from speech therapists and nutritionists.

Genetics

Documentation Requirements

Genetic counseling notes should document family history, potential syndromic associations, and any genetic testing performed.

Common Clinical Scenarios

Scenarios may include families seeking genetic counseling after a diagnosis of cleft lip, particularly if there are concerns about recurrence in future pregnancies.

Billing Considerations

Coders should consider the implications of genetic syndromes that may present with cleft lip, such as Van der Woude syndrome or 22q11.2 deletion syndrome.

Coding Guidelines

Inclusion Criteria

Use Q36.9 When
  • According to ICD
  • 10 coding guidelines, congenital conditions should be coded based on the specific malformation and any associated conditions
  • Documentation must support the diagnosis and any interventions performed

Exclusion Criteria

Do NOT use Q36.9 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

40650CPT Code

Repair of cleft lip

Clinical Scenario

Used for surgical repair of unilateral cleft lip in infants.

Documentation Requirements

Operative report detailing the procedure performed and any complications.

Specialty Considerations

Pediatric surgeons should document the surgical approach and any associated procedures.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of congenital conditions, improving the ability to capture the complexity of cases like unilateral cleft lip and associated anomalies.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of congenital conditions, improving the ability to capture the complexity of cases like unilateral cleft lip and associated anomalies.

Reimbursement & Billing Impact

The transition to ICD-10 has allowed for more specific coding of congenital conditions, improving the ability to capture the complexity of cases like unilateral cleft lip and associated anomalies.

Resources

Clinical References

  • •
    American Cleft Palate-Craniofacial Association

Coding & Billing References

  • •
    American Cleft Palate-Craniofacial Association

Frequently Asked Questions

What is the difference between unilateral and bilateral cleft lip?

Unilateral cleft lip affects one side of the lip, while bilateral cleft lip involves both sides. The surgical approach and potential complications may differ significantly between the two.