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ICD-10 Guide
ICD-10 CodesQ44.7

Q44.7

Billable

Other congenital malformations of liver

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q44.7 is a billable code used to indicate a diagnosis of other congenital malformations of liver.

Key Diagnostic Point:

Congenital malformations of the liver encompass a variety of structural anomalies that can significantly impact the digestive system and overall health of affected individuals. These malformations may include conditions such as biliary atresia, hepatic cysts, and other structural abnormalities that can lead to impaired liver function. In pediatric patients, these conditions often present with symptoms such as jaundice, abdominal distension, and failure to thrive. The liver plays a crucial role in digestion and metabolism, and congenital malformations can lead to complications such as cholestasis, portal hypertension, and liver failure. Diagnosis typically involves imaging studies such as ultrasound, CT scans, or MRI, alongside laboratory tests to assess liver function. Management may require surgical intervention, such as liver transplantation in severe cases, and ongoing medical care to monitor liver function and nutritional status. Understanding the implications of these malformations is essential for accurate coding and appropriate clinical management.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variety of congenital liver malformations with overlapping symptoms
  • Need for precise documentation of associated conditions
  • Potential for multiple coding scenarios based on severity and treatment
  • Variability in clinical presentation and diagnostic criteria

Audit Risk Factors

  • Inadequate documentation of the specific malformation
  • Failure to capture associated digestive system anomalies
  • Misclassification of severity or type of malformation
  • Lack of clarity in the treatment plan and outcomes

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Detailed clinical notes including growth parameters, symptoms, and treatment plans are essential for pediatric patients with congenital liver malformations.

Common Clinical Scenarios

Common scenarios include newborns presenting with jaundice, failure to thrive, or abdominal distension requiring further evaluation.

Billing Considerations

Pediatric coders must be aware of the developmental implications of liver malformations and their impact on growth and nutrition.

Genetics

Documentation Requirements

Genetic testing results and family history are crucial for understanding the etiology of congenital liver malformations.

Common Clinical Scenarios

Genetic counseling may be required for families with a history of congenital anomalies, including liver malformations.

Billing Considerations

Coders should consider the genetic syndromes associated with liver malformations, which may influence coding and management.

Coding Guidelines

Inclusion Criteria

Use Q44.7 When
  • Follow the official ICD
  • CM coding guidelines for congenital conditions, ensuring accurate documentation of the malformation type, associated symptoms, and any surgical interventions performed

Exclusion Criteria

Do NOT use Q44.7 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

44120CPT Code

Laparotomy with exploration of the liver

Clinical Scenario

Used in cases of suspected congenital liver malformations requiring surgical intervention.

Documentation Requirements

Operative reports detailing findings and interventions performed.

Specialty Considerations

Pediatric surgeons must document the specific malformation and any associated procedures.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of congenital liver malformations, improving the accuracy of data collection and reimbursement processes.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of congenital liver malformations, improving the accuracy of data collection and reimbursement processes.

Reimbursement & Billing Impact

reimbursement processes.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What are the common congenital liver malformations?

Common congenital liver malformations include biliary atresia, hepatic cysts, and congenital hepatic fibrosis. Each condition presents unique challenges in diagnosis and management, requiring careful coding to reflect the specific malformation.