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v1.0.0
ICD-10 Guide
ICD-10 CodesQ63.0

Q63.0

Billable

Accessory kidney

BILLABLE STATUSYes
IMPLEMENTATION DATEOctober 1, 2015
LAST UPDATED09/11/2025

Code Description

ICD-10 Q63.0 is a billable code used to indicate a diagnosis of accessory kidney.

Key Diagnostic Point:

Accessory kidney, also known as supernumerary kidney, is a congenital anomaly characterized by the presence of an additional kidney that is typically smaller than the normal kidneys. This condition arises during embryonic development when the metanephric blastema, which forms the kidneys, divides abnormally. Accessory kidneys may be located in the normal renal fossa or may be ectopic, situated in an unusual location such as the pelvis or thorax. While many individuals with an accessory kidney remain asymptomatic, some may experience complications such as urinary obstruction, infection, or hypertension. Diagnosis is often made through imaging studies such as ultrasound or CT scans, which can reveal the presence and location of the accessory kidney. Management may vary from observation to surgical intervention, depending on the symptoms and complications present. Understanding the implications of accessory kidneys is crucial in pediatric care, as these anomalies can be associated with other congenital malformations of the urinary system, including renal agenesis, polycystic kidney disease, and bladder exstrophy.

Code Complexity Analysis

Complexity Rating: Medium

Medium Complexity

Complexity Factors

  • Variability in presentation and symptoms of accessory kidneys
  • Potential association with other congenital urinary anomalies
  • Need for precise imaging documentation
  • Differentiation from other renal anomalies

Audit Risk Factors

  • Inadequate documentation of imaging studies
  • Failure to note associated congenital anomalies
  • Misclassification of accessory kidney as a normal variant
  • Lack of clarity in the clinical significance of the accessory kidney

Specialty Focus

Medical Specialties

Pediatrics

Documentation Requirements

Pediatric documentation should include detailed descriptions of symptoms, imaging results, and any associated congenital anomalies. Growth and developmental assessments may also be relevant.

Common Clinical Scenarios

Common scenarios include a child presenting with recurrent urinary tract infections or hypertension, where imaging reveals an accessory kidney.

Billing Considerations

Coders should be aware of the potential for associated urinary tract anomalies and ensure that all relevant conditions are documented and coded.

Genetics

Documentation Requirements

Genetic documentation should include family history, any syndromic associations, and results from genetic testing if applicable.

Common Clinical Scenarios

Scenarios may involve genetic counseling for families with a history of congenital kidney anomalies or syndromes associated with renal malformations.

Billing Considerations

Consideration should be given to the potential genetic syndromes that may present with accessory kidneys, necessitating thorough documentation.

Coding Guidelines

Inclusion Criteria

Use Q63.0 When
  • According to ICD
  • 10 guidelines, congenital conditions like accessory kidneys should be coded based on the specific anatomical and clinical findings
  • Coders must ensure that the diagnosis is supported by appropriate documentation, including imaging and clinical assessments

Exclusion Criteria

Do NOT use Q63.0 When
No specific exclusions found.

Related ICD-10 Codes

Related CPT Codes

50360CPT Code

Nephrectomy, partial

Clinical Scenario

Used when surgical intervention is required for symptomatic accessory kidney.

Documentation Requirements

Document indications for surgery, imaging findings, and pre-operative assessments.

Specialty Considerations

Pediatric surgeons should provide detailed operative notes to support the procedure.

ICD-10 Impact

Diagnostic & Documentation Impact

Enhanced Specificity

ICD-10 Improvements

The transition to ICD-10 has allowed for more specific coding of congenital conditions like accessory kidneys, improving the accuracy of data collection and reimbursement processes.

ICD-9 vs ICD-10

The transition to ICD-10 has allowed for more specific coding of congenital conditions like accessory kidneys, improving the accuracy of data collection and reimbursement processes.

Reimbursement & Billing Impact

reimbursement processes.

Resources

Clinical References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Coding & Billing References

  • •
    ICD-10-CM Official Guidelines for Coding and Reporting

Frequently Asked Questions

What is the clinical significance of an accessory kidney?

An accessory kidney may be asymptomatic but can lead to complications such as urinary obstruction or infection. It is essential to monitor renal function and assess for any associated urinary tract anomalies.