Cloacal exstrophy of urinary bladder
ICD-10 Q64.12 is a billable code used to indicate a diagnosis of cloacal exstrophy of urinary bladder.
Cloacal exstrophy is a rare congenital malformation characterized by a failure of the normal closure of the abdominal wall and the formation of the cloaca, which is a common cavity for the urinary, reproductive, and gastrointestinal tracts. In this condition, the urinary bladder is exposed and may be split into two parts, leading to significant urinary and reproductive complications. Patients often present with associated anomalies such as renal agenesis, bladder exstrophy, and other urinary tract malformations. The condition is typically diagnosed at birth through physical examination and imaging studies. Management often requires a multidisciplinary approach, including surgical intervention to reconstruct the urinary tract and bladder, as well as ongoing urological care. Long-term follow-up is essential to monitor for complications such as urinary incontinence, recurrent urinary tract infections, and renal function impairment. Genetic counseling may also be indicated due to the potential association with chromosomal abnormalities and syndromic presentations.
Detailed birth history, physical examination findings, and surgical intervention records are essential for accurate coding.
Common scenarios include newborns presenting with cloacal exstrophy, requiring immediate surgical intervention and long-term urological follow-up.
Coders must be aware of the potential for associated congenital anomalies and ensure all are documented and coded appropriately.
Genetic testing results, family history, and any syndromic associations must be documented to support coding.
Genetic counseling sessions for families with a history of cloacal exstrophy or related conditions.
Consideration of chromosomal abnormalities that may be associated with cloacal exstrophy is crucial for accurate coding.
Used for evaluation of urinary tract anomalies in patients with cloacal exstrophy.
Document indications for cystoscopy and findings.
Pediatric urologists often perform this procedure.
Cloacal exstrophy is a rare congenital condition where the urinary bladder is exposed due to a failure of the abdominal wall to close properly. It often presents with associated urinary and reproductive tract anomalies.
