Congenital absence and malformations of spleen
ICD-10 Q89.0 is a billable code used to indicate a diagnosis of congenital absence and malformations of spleen.
Congenital absence and malformations of the spleen encompass a range of conditions where the spleen is either absent (asplenia) or malformed. These anomalies can occur as isolated defects or as part of syndromic presentations, often associated with other congenital malformations. The spleen plays a crucial role in the immune system, particularly in filtering blood and managing immune responses. Asplenia can lead to increased susceptibility to infections, particularly from encapsulated bacteria. Malformations may include accessory spleens or ectopic spleens, which can complicate surgical interventions or lead to functional impairments. Diagnosis typically involves imaging studies such as ultrasound or MRI, and management may require immunizations and prophylactic antibiotics to mitigate infection risks. Understanding the implications of these conditions is essential for pediatric care, as they can significantly impact a child's health and development.
Pediatric documentation must include growth parameters, immunization status, and any infections or complications related to splenic absence.
Common scenarios include a newborn diagnosed with asplenia during routine examination or a child presenting with recurrent infections.
Coders should be aware of the implications of splenic absence on immunization schedules and the need for prophylactic antibiotics.
Genetic documentation should include family history, genetic testing results, and any syndromic associations.
Scenarios may involve genetic counseling for families with a history of congenital malformations or syndromes associated with asplenia.
Consideration of chromosomal abnormalities that may co-occur with splenic malformations is crucial for accurate coding.
Used to evaluate spleen size and presence in suspected congenital absence.
Document findings related to spleen morphology and any associated anomalies.
Pediatric ultrasound protocols may differ from adult protocols.
Coding Q89.0 indicates a congenital absence or malformation of the spleen, which has significant implications for patient management, including increased risk of infections and the need for specific immunizations and follow-up care.
