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v1.0.0
ICD-10 Guide
DiagnosesAutoimmune Hepatitis

Autoimmune Hepatitis

ICD-10 Coding for Autoimmune Hepatitis(K75.4)

PRIMARY SPECIALTYGastroenterology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Autoimmune Hepatitis?
Essential facts and insights about Autoimmune Hepatitis

Key Clinical Considerations:

  • Fatigue, jaundice, abdominal discomfort
  • Elevated liver enzymes (ALT, AST), positive autoantibodies (ANA, SMA, LKM-1)
  • Hepatomegaly, signs of liver failure (ascites, spider angiomata)

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history, physical examination findings, lab results
  • ICD-10-CM codes for autoimmune hepatitis (K75.2)
  • Examples: 'Patient presents with jaundice and elevated ALT/AST levels.'

Coding Guidelines

Usage Guidelines & Examples

  • Follow ICD-10 guidelines for specificity.
  • Common errors include incorrect coding of liver diseases.

Code Exclusions

Important Exclusions

  • Viral hepatitis, alcoholic liver disease
  • K75.1 (Autoimmune hepatitis, unspecified)

Related ICD-10 Codes

Primary Codes
K75.2
Autoimmune hepatitis
Ancillary Codes
K74.3
I85.01
Differential Codes
B18.1
K70.30

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Gastroenterology

Specialty Applications

  • Adults and children with autoimmune disorders
  • Outpatient and inpatient gastroenterology settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

Documentation requirements?

Include detailed patient history, lab results, and physical exam findings.

Billing considerations?

Ensure accurate coding and documentation to support medical necessity.