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v1.0.0
ICD-10 Guide
DiagnosesPrimary Biliary Cholangitis

Primary Biliary Cholangitis

ICD-10 Coding for Primary Biliary Cholangitis(K83.0, K74.3)

PRIMARY SPECIALTYHepatology
COMPLEXITYHigh
LAST UPDATED09/15/2025
Sam Tuffun, PT, DPT
Physical Therapist | Medical Coding & Billing Contributor

Diagnosis Overview

What is Primary Biliary Cholangitis?
Essential facts and insights about Primary Biliary Cholangitis

Key Clinical Considerations:

  • Fatigue
  • Pruritus
  • Jaundice
  • Elevated alkaline phosphatase levels
  • Presence of antimitochondrial antibodies (AMA)

Clinical Information

Clinical Criteria & Documentation Requirements

  • Patient history including symptoms and duration
  • Results of liver function tests and imaging studies
  • Confirmation of AMA positivity
  • Assessment of liver biopsy if performed

Coding Guidelines

Usage Guidelines & Examples

  • Follow guidelines for coding chronic liver diseases.
  • Common errors include misclassifying the condition or omitting AMA testing results.

Code Exclusions

Important Exclusions

  • Secondary biliary cholangitis
  • Autoimmune hepatitis
  • Other liver diseases

Related ICD-10 Codes

Primary Codes
K74.3
Primary biliary cholangitis
Ancillary Codes
R94.5
R18.0
Differential Codes
K74.3
K83.0

Related CPT Codes

CPT codes will be available in a future update.

Specialty Focus

Primary Specialty

Hepatology

Specialty Applications

  • Adults, primarily women aged 40-60
  • Hepatology clinics and outpatient settings

Coding Complexity

High Complexity

This diagnosis requires careful attention to:

  • Comprehensive clinical documentation
  • Accurate code selection based on clinical criteria
  • Proper exclusion considerations
  • Specialty-specific coding guidelines

Documentation

Documentation Templates

Billing Information

Billing Considerations

  • Ensure proper documentation for billing
  • Verify code specificity requirements
  • Check for any additional codes needed
  • Review payer-specific guidelines

Common Issues

  • Insufficient clinical documentation
  • Incorrect code selection
  • Missing supporting diagnoses
  • Timing and frequency documentation

Frequently Asked Questions

What are the documentation requirements?

Document clinical symptoms, lab results, and any imaging findings.

What are the billing considerations?

Ensure accurate coding of primary biliary cholangitis and related tests.